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정종윤 ( Jong Yun Cheong ),김성일 ( Sung Il Kim ),박찬원 ( Chan Won Park ),이창훈 ( Chang Hun Lee ),김인주 ( In Joo Kim ),곽임수 ( Ihm Soo Kwak ),김용기 ( Yong Ki Kim ),나하연 ( Ha Yeon Rha ) 대한류마티스학회 2001 대한류마티스학회지 Vol.8 No.1
Dermatomyositis is an autoimmune connective tissue disorder characterized by symmetrical proximal muscle weakness due to chronic inflammation and degeneration of skeletal muscle. Cancer occurs in patients with dermatomyositis with a frequency estimated between 15-20%. The common sites of malignancy are stomach, breast, ovary, lung and etc. The cases that have been reported so far are dermatomyositis associated with lymphoproliferative disorder and cancer of colon, liver, pancrease, pharynx, uterine cervix, testis, kidney. But dermatomyositis associated with thyroid cancer has not been reported in Korea. We, the authors, experienced a case of dermatomyositis associated with the thyroid cancer and as such we are reporting the case with literature reviews.
성인 급성 골수성 백혈병의 염색체 이상과 면역 표현형의 임상적 중요성
조군제(Goon Jae Cho),공옥녀(Ok Nyu Kong),정종윤(Jong Yun Cheong),이경우(Kyung Woo Lee),이정현(Jung Hyun Lee),정주섭(Joo Seop Chung),이은엽(Eun Yup Lee) 대한내과학회 2002 대한내과학회지 Vol.62 No.6
Background : This study was performed to identify the incidence and prognostic significance of chromosomal abnormalities as well as clinical significance of immuno phenotype in patients with acute myelogenous leukemia (AML). Methods : The chromosomal abnormalities, immunophenotype and their hematologic/clinical correlations were studied in 68 patients with de novo AML admitted to Pusan National University Hospital between January 1996 and December 2000. 47 of 68 patients had received induction chemotherapy and we analysed the response of treatment according to the karyotype pattern and immunophenotype. Results : The karyotypic patterns were divided into three groups; favorable (t (8;21), t (15;17) and inv (16); n=19,28%), poor (-5, del (5q), -7, der (1;7), abn (3q) and complex karyotypes; n=11, 16%) and intermediate group (other abnormalities or normal karyotype; n=38, 56%). The incidence of chromosomal abnormalities was 56% (38/68) and overall complete remission (CR) rate of 47 evaluable patients was 64%. The CR rates of favorable, intermediate and poor groups were 88%, 59% and 44%, respectively (p=0.021). The median survival time of all patients was 7 months, those of poor and intermediate groups being 2 months and 6 months. The median survival time of favorable group was not reached (p=0.008). The overall 5 year survival rate was 38% and those of favorable, intermediate and poor groups were 68%, 31% and 9%, respectively (p=0.009). Expression of CD7, CD14, CD33, CD34 and terminal deoxynucleotidyl transferase had no impact on CR rate and overall survival. In multivariate analysis, both age and chromosomal abnormalities influence significantly on prognosis. Conclusion : Cytogenetic study is important in predicting the outcome of patients with AML. And the treatment must be tailored according to the result of cytogenetics such as this study.(Korean J Med 62:608-616, 2002)
박정래(Jung Lae Park),이동현(Dong Hyun Lee),강진욱(Jin Ouk Kang),정종윤(Jong Yun Cheong),박혜경(Hye Kyung Park),공옥녀(Ok Nyu Kong),손석만(Seok Man Son),김인주(In Joo Kim),김용기(Yong Ki Kim) 대한내과학회 2002 대한내과학회지 Vol.63 No.3
We experienced a Korean patient with complete form of pachydermoperiostosis. He presented with typical features consisting of clubbing with spade like enlargement of the hand and feet, thickening of facial skin and scalp, irregular thickening of cortex with periosteal new bone formation involving radii, ulnae, tibiae, and fibulae. Classically, pachydermoperiostosis is characterized by a triad of finger clubbing, periostitis, skin and soft tissue changes, giving an acromegaloid look. A variety of associated abnormalities have been described such as cranial suture defects, female escutcheon, bone marrow failure. There are a few reports documenting gastric ulcer, hypertrophic gastropathy and Crohn's disease as accompanying diseases. The patient had upper gastrointestinal bleeding caused by hemorrhagic gastritis and duodenal ulcer. A case is herein reported of pachydermoperiostosis accompanied by peptic ulcer disease.(Korean J Med 63:329-334, 2002)