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심찬섭,이영숙,현창옥,최진수,이진관,서석조,이동화 ( Chan Sup Sim,Young Sook Lee,Chang Ok Hyun,Jin Soo Choi,Jin Kwan Lee,Succ Jo Suh,Dong Hwa Lee ) 대한소화기학회 1980 대한소화기학회지 Vol.12 No.1
Gilberts syr.drome is a condition which has been called idiopathic unconjugated hyperbili rubinemia, constitutional hepatic dysfuction or familial non-hemolytic jaundice with the characteristics of a benign, persistent but variable elevation of the plasma unconjugated bilirubin. A 2g-year old Korean male was admitted due to intermittent jaundice, indigestion, and general malaise. Physical examination revealed icteric sclera, but no hepatosplenmegaly. Laboratory findings showed increased serum bilirubin with indirect reacting bilirubin predo- minating. Percutaneous needle biopsy specimen of liver showed no special abnormalities. Calory deprivation test with caloric intake of 400 Cal a day for 72 hours resulted in a significant increase in the plasma bilirubin concentration (especially indirect form) in this patient. A brief review of the pertinent literature was made.
박찬욱,김진홍,이준성,문철,이동화,이문성,조성원,심찬섭,문수남 대한소화기내시경학회 1993 Clinical Endoscopy Vol.13 No.1
Choledochal cyst is a relatively rare disease entity considered to be a congenital cyatic dilatation of the common bile duct. Since occurrence of malignant tumor in choledochal cyet was firat reported by Irwin and Morrison in 1944, approximately 100 more cases of malignant tumors arising in congenital choledocal cyst have been reported in the world, and the risk of malignant tumor related to choledochal cyst have been reported 2.4-14%. Recently, we experienced a case of adenocarcinoma arising in choledochal cyst in 39 year-old woman who was diagnosed by ERCP and cholangioscopy with forceps biopsy, and was treated with en bloc resection of the choledochal cyst along with the pancreatic head and duodenum.