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이정상,김용일,김성권,안규리,김순배,이근후 대한내과학회 1986 대한내과학회지 Vol.31 No.2
A clinicopathologic study for 142 patients of IgA nephropathy has been performed in a series of 410 specimens of renal biopsy, which were examined by light microscopy and immunoflorescent study since Jan, 1979 until Feb. 1985. The results were as followings; 1) IgA nephropathy was 34.6% of primary glomerulonephritis. 2) Mean age of the population was 29.5 years, and 72.6% were distributed between 15 to 35 years. Male to female ratio was 1.2:l. 3) The most common clinical syndrome was asyrnptomatic urinary abnormality(41. 5%), then nephrotic syndrome, chronic glomerulonephritis, acute nephritis and RPGN in that order. Gross hematuria has occurred in 66.2% of the cases including 31.7% of recurrent gross hematuria. The onset followed recent URI-like symptoms in 43. 7% of the cases, 4) Significant proteinuria($gt;1. g/day) noted in 49.2% including 10.9% of nephroticrange proteinuria. Azotemia(serum creatinine $gt; 1, 7 mg/dl) was noted in 23. 9% and serum IgA was elevated in 53. 1%. 5) Of the pathologic grading according to ISKDC classification of Henoch-Schonlein nephritis, the most common findings was grade III in which less than 50% of glomeruli is affected by crescents or segmental lesions, then grade I, V, IV, II , VI in that order, 6) IgA was found unassociated with other immunoglobulin in 31, 7%; with IgG in 50.7%; with IgM in 33.1%. 7) 16.7% of the cases progressed to deterioration of renal function in follow-up of mean 11.7 months. 8) Proteinuria, hypertension and initial azotemia, but not gross hematuria, had significant correlation with pathologic grading and prognosis.
신이식에 합병된 Rhinocerebral Mucormycosis 1 예
한진석,이정상,김성권,지제근,이상구,김순배,이근후,김윤권 대한내과학회 1987 대한내과학회지 Vol.32 No.2
We reported a case of 29year old kidney transplant recipient male who was diagnosed as rhinocerebral mucormycosis confirmed by nasal turbinate biopsy and brain CT. He complained of right eyeball pain, right facial swelling, diplopia, right facial palsy developed after immunosuppressive therapy which was done under the impression of rejection. Physical examination revealed pale, hypertrophic nasal mucosa and blood clot on ulceration and bone exposure on the anterior portion of right middle turbinate. Filamentous mycelia, consisting of distinctively broad, thin walled, non-septate, rather irregular hypae which tend to branch at righf angle, was found on the nasal biopsy. Brain CT revealed thickening of right maxillary sinus mucosa with right side turbinate hypertrophy and right exophthalmos, but definite retrobulbar mass or evidence of cavernous sinus thrombosis was not found. His symptom except right facial palsy was relieved with the treatment of amphotericin B and flucytosine.