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원종훈 ( Jong Hoon Won ),박준수 ( Joon Soo Park ),정현 ( Hyun Chung ),장효찬 ( Hyo Chan Jang ) 대한피부과학회 2009 大韓皮膚科學會誌 Vol.47 No.8
Background: Many different dermatologic manifestations can accompany a variety of systemic diseases such as rheumatic disorders. The number of patients who have skin lesions related to systemic diseases is steadily increasing. In such cases, dermatologic consultation can be important to diagnosis and treatment. Objective: The purpose of this study was to analyze patterns of skin manifestations in rheumatic diseases. Methods: We did an analysis of data for 192 inpatients who were referred by the department of rheumatology and consulted by the department of dermatology between May 1, 2005 and April 30, 2009. We retrospectively reviewed their medical records and noted age, sex, reasons for dermatologic consultation, diagnosis of the dermatoses and changed diagnosis after the consultation. Results: The percent of patients who were referred by the department of rheumatology and consulted by the department of dermatology was 15.5% (192 consulted inpatients/1,242 rheumatologic inpatients). The most frequent age group was those in their 5th decade of life (23.0%) and the male to female ratio was 1:2.15. Consultations for dermatologic manifestations unrelated to systemic or rheumatic diseases were the most common reason for consultation (62.0%). Dermatoses related to systemic or rheumatic diseases were the 2nd most common reason of consultation (34.9%). Infectious diseases were the most common dermatoses (46 cases). There were 13 cases where there was a diagnosis of undetermined dermatoses and changed diagnosis after dermatologic consultation. Conclusion: Analysis of consultations from inpatients referred by the department of rheumatology to the department of dermatology indicates that there is a substantial number of patients that have skin manifestations of their rheumatic diseases. (Korean J Dermatol 2009;47(8):891~895)
원종훈 ( Jong Hoon Won ),현동녘 ( Dong Nyeok Hyun ),박준수 ( Joon Soo Park ),정현 ( Hyun Chung ) 대한피부과학회 2008 대한피부과학회지 Vol.46 No.6
Angiokeratoma of Fordyce is a relatively common type of angiokeratoma that is characterized by small, multiple, purplish to dark red papules on the scrotum. Pathogenesis is unknown, but it has been suggested that increased venous pressure caused by varicocele, hernia or tumor of the epididymis can induce angiokeratoma of Fordyce. We report a case of unilateral angiokeratoma of Fordyce with varicocele in a 30 year-old man. He presented with approximatly 2 mm sized, purplish to dark red, and multiple hyperkeratotic papules on the left scrotum. The lesions were strictly limited to the left side of the scrotum and associated with varicocele on the same side. Histopathologically, hyperkeratosis, acanthosis with elongation of rete ridges and dilated papillary vessels are presented. Based on this clinical and histologic finding, we diagnosed this case as unilateral angiokeratoma of Fordyce with varicocele. The patient was treated with varicocelectomy for left varicocele and then cryotherapy for skin lesions. (Korean J Dermatol 2008;46(6):831∼834)
가성가성 부갑상선 기능저하증 환자에서 발생한 올브라이트 유전성 골이영양증 2예
원종훈 ( Jong Hoon Won ),현동녘 ( Dong Nyeok Hyun ),박준수 ( Joon Soo Park ),정현 ( Hyun Chung ),정의달 ( Eui Dal Jung ) 대한피부과학회 2009 대한피부과학회지 Vol.47 No.7
A 36 year-old man and his 6 month-old daughter presented with multiple, slightly depressed, skin-colored, hard nodules and plaques on the abdomen, back, and both extremities. They also showed abnormal physical appearance, including short stature and neck, round face, and short digits, which suggested Albright`s hereditary osteodystrophy (AHO). Histopathologically, various sized bony spicules were present in the dermis. The laboratory results showed normal serum calcium, phosphorus and parathyroid hormone levels. On the basis of clinical, laboratory and histologic findings, we diagnosed these cases as Albright`s hereditary osteodystrophy with cutaneous ossification occurring in pseudopseudohypoparathyroidism. (Korean J Dermatol 2009;47(7):820~824)
A Maximum Likelihood Estimator Based Tracking Algorithm for GNSS Signals
원종훈(Jong-Hoon Won),Thomas Pany,Bernd Eissfeller 한국항해항만학회 2006 한국항해항만학회 학술대회논문집 Vol.2 No.-
This paper presents a novel signal tracking algorithm for GNSS receivers using a MLE technique. In order to perform a robust signal tracking in severe signal environments, e.g., high dynamics for navigation vehicles or weak signals for indoor positioning, the MLE based signal tracking approach is adopted in the paper. With assuming white Gaussian additive noise, the cost function of MLE is expanded to the cost function of NLSE. Efficient and practical approach for Doppler frequency tracking by the MLE is derived based on the assumption of code-free signals, i.e., the cost function of the MLE for carrier Doppler tracking is used to derive a discriminator function to create error signals from incoming and reference signals. The use of the MLE method for carrier tracking makes it possible to generalize the MLE equation for arbitrary codes and modulation schemes. This is ideally suited for various GNSS signals with same structure of tracking module. This paper proposes two different types of MLE based tracking method, i.e., an iterative batch processing method and a non-iterative feed-forward processing method. The first method is derived without any limitation on time consumption, while the second method is proposed for a time limited case by using a 1st derivative of cost function, which is proportional to error signal from discriminators of conventional tracking methods. The second method can be implemented by a block diagram approach for tracking carrier phase, Doppler frequency and code phase with assuming no correlation of signal parameters. Finally, a state space form of FLL/PLL/DLL is adopted to the designed MLE based tracking algorithm for reducing noise on the estimated signal parameters.