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이용원,이영곤,현명수,김종설,박화종,최진명 대한내과학회 1987 대한내과학회지 Vol.33 No.1
lmmunoglobolin-related or primary amyloidosis has been reported to develop in 6 to 15% of patients with multiple myeloma and especially in 20 to 24% of patients with light chain myeloma. The amyloid in such patients is composed of monoclonal light chains or their fragments. These Bence-Jones proteins become polymerized to form amyloid either directly or after partial degradation by associated macrophages. A 54-year-old female patient was admitted to the Yeungnam University Hospital due to general weakness and yellowish-brown, grouped papules on the lips, neck, and both forearms. She was treated with melphalan and prednisone. She exhibited remarkable clinical improvement concomitant with marked reduction in proteinuria and reduction in cutaneous amyloid deposition. A case of amyloidosis associated with light chain myeloma is reported with review of the literatures.