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이도경 ( Do Kyung Lee ),허성혁 ( Sung Hyuk Heo ),박기정 ( Key Chung Park ),안태범 ( Tae Beom Ahn ),윤성상 ( Sung Sang Yoon ),정경천 ( Kyung Cheon Chung ),장대일 ( Dae Il Chang ) 경희대학교 경희의료원 2010 慶熙醫學 Vol.26 No.1
Ovarian hyperstimulation syndrome (OHSS) is a potentially serious complication occurring in ovarian induction therapy. We report a case of ischemic stroke with OHSS. Previously healthy 33-year-old woman underwented In vitro fertilization-Embryo transfer (IVF-ET) 6 days ago. She admitted for dyspnea and abdominal distension. Chest X-ray arid simple abdomen showed massive pleural effusion and ascites. Left hemiparesis and sensory extinction were developed suddenly 2days after admission. She was administrated with recombinant tissue-plasminogen activator (rt-PA) intravenously witin 3hours of symptom onset. Hemiparesis was improved remarkably after rt-PA infusion. Magnetic resonance imaging showed acute ischemic infarction on the right basal ganglia, corona radiata, temporal lobe and parietal lobe, and left frontal lobe, and parietal lobe. Laboratory studies showed Hemoconcentration (hematocrit: 50.4%), elevated D-dimer and fibrinogen (5.03 μg/mL and 406 mg/dL respectively) and decreased protein S activity (51%). 20 days after admission, she discharged without neurologic sequelae. Screening test for hypercoagulable state should be considered before ovulation induction therapy to prevent cerebrovascular complication with OHSS.
운동신경원성 질환을 동반한 전두측두엽치매의 임상양상과 신경심리소견
박기정,정용,김은주,진주희,강수진,나덕렬 대한치매학회 2003 Dementia and Neurocognitive Disorders Vol.2 No.1
Backgrounds:Frontotemporal dementia (FTD) is rarely associated with motor neuron disease (MND). This comorbidity (FTD-MND), a subtype of FTD, results in progressive dementia and muscle weakness. Among the few available reports of series of patients, however, there have been controversies about the clinical course of FTD-MND. This study, the first report of a series of FTD-MND patients in Korea, investigated demographic and clinical features, clinical course, and neuropsychological findings of nine patients with FTD-MND. Methods:Nine FTD-MND patients (2 men and 7 women with mean age 55.6±7.2 years) were selected among 45 FTD patients who met the FTD criteria proposed by the Lund and Manchester Groups. Their clinical and neuropsychological findings were analyzed retrospectively. Results:Mean age of onset was 54.3±8.0 years. The time interval from onset to death was 27±11.3 months. Presenting symptoms were personality change, hyperphagia, nonfluent speech or motor weakness. In most cases (8/9), dementia preceded the muscle weakness;in only one patient the muscle weakness preceded the cognitive decline. Regarding the muscle weakness, bulbar symptoms occurred earlier than limb weakness in four patients;bulbar and limb weakness occurred simultaneously in another four patients;in the remaining one patient limb weakness preceded bulbar weakness. Neuropsychologic tests showed no specific patterns but diffuse dysfunction in all cognitive domains. Conclusions:Our study suggests that FTD-MND predominantly affects the bulbar muscles rather than the limb muscles in early stage and symptoms related to MND occurs later than those related to FTD. The time from diagnosis to death was 10.6±6.5 months, suggesting that FTD-MND is a rapidly progressive disease. This rapid clinical course may account for our neuropsychological findings that showed general cognitive deficits father than predominant frontal dysfunctions.
좌측 전두엽 뇌경색 환자에서 생긴 초피질 감각 실어증 1예
박기정,윤성상,윤강욱,서미경,나덕렬,장대일 대한치매학회 2003 Dementia and Neurocognitive Disorders Vol.2 No.1
Motor aphasia is usually associated with anterior lesions of dominant hemisphere whereas sensory aphasia is associated with posterior lesions. Exceptional cases, however, have rarely been reported. We report a 78-year-old right-handed woman who showed transcortical sensory aphasia of acute onset. The brain MRI showed an infarction in left superior frontal gyrus and middle frontal gyrus. SPECT revealed more extensive lesions in the left frontal lobe and basal ganalia. These results suggest that dominant frontal lobe mediates auditory comprehension in rare cases.
Transient Global Amnesia with Transient Ischemic Attack in the Habenular Nucleus
Heo, Sung Hyuk,Park, Key Chung,Yoon, Sung Sang,Ahn, Tea Beom,Chang, Dae Il,Chung, Kyung Cheon 경희대학교 2006 慶熙醫學 Vol.22 No.1
일과성 전기억상실증은 최근 확산강조 자기공명영상에서 관찰되는 해마의 허혈성 변화로 가장 많이 보고되어 있으나 그 기전은 아직까지 명확히 밝혀져 있지 않다. 우리는 기억과 학습의 중요한 기능을 하는 것으로 알려진 고삐핵의 일과성허혈발작에 의한 일과성 전기억상실증을 경험하여 보고하는 바이다. 환자는 증상발현 7시간과 96시간 이후에 연속적으로 확산강조 자기공명영상을 시행하였고, 처음 영상에서 나타난 고삐핵의 매우 작은 고신호강도 병변이 이후 영상에서는 관찰되지 않았다. The TGA can be produced by the small and discrete thalamic structure like habenular nucleus that is thought to be related with the cholinergic network for learning and memory in the central nervous system.