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Her, Sun Mi,Lee, Keum Hwa,Shin, Jae Il Korean Society of Pediatric Nephrology 2017 Childhood kidney diseases Vol.21 No.2
Focal segmental glomerulosclerosis (FSGS) in children, which is a kind of nephrotic syndrome showing steroid resistance, usually progresses to a substantial number of end stage renal disease (ESRD). Although the pathogenesis of primary FSGS is unclear, several recent studies have reported that FSGS is associated with circulating immune factors such as soluble urokinase-type plasminogen activator receptor (suPAR) or anti-CD40 autoantibody. We report a successfully treated case of a 19-year-old female patient who experienced a recurrence of primary FSGS. After the diagnosis of FSGS, the patient progressed to ESRD and received a kidney transplantation (KT). Three days later, recurrence was suspected through proteinuria and hypoalbuminemia. She has been performed plasmapheresis and high dose methylprednisolone pulse therapy and shown remission status without increasing proteinuria for four years after KT. In conclusion, strong immunosuppressive therapy may be helpful for a good prognosis of recurrent FSGS, suppressing several immunologic circulating factors related disease pathogenesis.
Her, Sun Mi,Lee, Keum Hwa,Kim, Ji Hong,Lee, Jae Seung,Kim, Pyung Kil,Shin, Jae Il Korean Society of Pediatric Nephrology 2017 Childhood kidney diseases Vol.21 No.2
Purpose: The American Society for Apheresis provides clinical guidelines for therapeutic apheresis in adults, but there are no guidelines for children. This study aimed to analyze the effect of therapeutic plasma exchange (TPE) in pediatric patients with various kidney diseases in Korea. Methods: We retrospectively reviewed the data of 16 children (up to 18 years of age) who were admitted to Severance Children's Hospital with refractory kidney disease. All patients received TPE between 1994 and 2016. Clinical and laboratory characteristics such as age, weight, sex, change in blood urea nitrogen (BUN), and creatinine level before and after TPE, and complications after TPE were analyzed. Results: The mean age and weight of the 16 patients at the time of TPE was $11.3{\pm}4.0$ years and $34.6{\pm}17.5$ kg, respectively. The BUN level was 35.4 mg/dL before TPE and significantly decreased to 21.5 mg/dL (P=0.025) at 1 week and 20.5 mg/dL (P= 0.01) at 1 month after TPE. The creatinine level significantly decreased from 1.20 mg/dL before TPE to 0.90 mg/dL (P=0.02) at 1 week after TPE. Four complications (hypovolemia, anemia, hypocalcemia, and thrombocytopenia) were reported, but were not fatal. Conclusion: Our findings suggest that TPE is an effective therapeutic modality in children with refractory kidney disease and can be indicated for the treatment of various kidney diseases.
An event of gm peppers tolerant to pepper mottle virus (PepMoV)
Eun-Mi Jeon,Sun-Hee Shin,Jung-Mi Park,Soon-Ho Choi,Dong-Bo Shim,Nam-Han Her,Jang-Ha Lee,Min Jung,Ki-Hyun Ryu,Soon-Chun Jeong,Chee-Hark Harn 한국육종학회 2013 한국육종학회 심포지엄 Vol.2013 No.07
In Korea, CMV (cucumber mosaic virus) is the most frequently occurring virus with a single infection rate of 45%. However, a total occurrence of CMV by co-infection, either couple or multiple, with BBWV (broad bean wilt virus), PepMoV (pepper mottle virus) and PMMoV (pepper mild mottle virus) covers over 90% in the field cultivation of pepper. The PepMoV is transmitted by several aphid species, and it has been considered the most frequently detected potyvirus when it co-infects with CMV or PMMoV. Since F1 hybrid that resistant to PepMoV has not been developed, we have developed transgenic peppers using Agrobacterium-mediated transformation with a Hc-Pro gene of the PepMoV. A large number of T1 peppers were tested for resistance to the PepMoV, and T1 peppers tolerant of PepMoV were selected. After consequent self-crossing up to T4 generation, highly tolerant peppers to PepMoV were selected. So far, BC3F1 lines have been selected by back-crossing with 4 elite lines through a breeding program. The horticultural differences of the GM line comparing to inbred lines were investigated and no statistical significance between GM and non-GM lines was found. Based on molecular analysis, One of GM lines, 10-2, contained the transgene in the non-coding region indicating that this line would be a GM event.
Recent Progress of PepMoV Resistant GM Pepper
Eun Mi Jeon,Sun Hee Shin,Soon Ho Choi,Dong Bo Shim,Nam Han Her,Jang Ha Lee,Min Jung,Ki Hyun Ryu,Soon-Chun Jeong,Chee Hark Harn 한국육종학회 2014 한국육종학회 심포지엄 Vol.2014 No.07
The PepMoV has been considered the most frequently detected potyvirus. When it co-infects with CMV or PMMoV, it gives severe impact to total pepper harvest in Korea. Since F1 hybrid that resistant to PepMoV has not been developed, we have developed transgenic peppers using Agrobacterium-mediated transformation with a Hc-Pro gene of the PepMoV. A large number of GM peppers were tested for resistance to the PepMoV, and after consequent self-crossing up to T4 generation, a highly tolerant pepper to PepMoV called T20 was selected. So far, BC4F1 lines have been selected by back-crossing with 4 elite lines through a breeding program. Very recently, based on molecular analysis, we have selected another event, #10-2, which is also resistant to PepMoV. Horticultural difference was investigated for both GM lines, #T20 and 10-2, and no significance was found comparing to non-GM lines.
Lee Mi-Yeon,Lee Jang-Ha,Ahn Hong-Il,Yoon Ju-Yeon,Her Nam-Han,Choi Jang-Kyung,Choi Gug-Seon,Kim Do-Sun,Harn Chee-Hark,Ryu Ki-Hyun The Korean Society of Plant Pathology 2006 Plant Pathology Journal Vol.22 No.3
Cultivated hot pepper crops showing severe mosaic symptom were found in Korea in 2004 and their causal agent was identified as Cucumber mosaic virus (CMV). These pepper crops was resistant to the virus in the filled, and they belonged to pathotype 0 (P0) resistant pepper. Resistance screening of selected pepper plants showed that a pepper isolate of CMV was the P0 resistance-breaking virus. This P0 resistance-breaking isolate of CMV, named as Ca-P1, was isolated from leaves of the virus-infected Capsicum annuum cv. Manidda that showed systemic severe mosaic symptom. Ca-P1-CMV could induce systemic mosaic symptoms on P0-susceptible (P0-S) and P0-resistant (P0-R) cultivars whereas an ordinary strain (Fny-CMV) could not infect P0-R. This result suggests that Ca-P1-CMV can overcome P0 resistant pepper cultivars. To analyze its genome sequence, the complete nucleotide sequence of RNA3 of Ca-P1-CMV was determined from the infectious full-length cDNA clone of the virus. RNA3 of Ca-P1-CMV consisted of 2,219 nucleotides. Overall sequence homology of RNA3-encoded two viral proteins (movement protein and coat protein) revealed high similarity (75.2-97.2%) with the known CMV strains. By sequence analysis with known representative strains of CMV, Ca-P1-CMV belongs to a typical member of CMV subgroup IB. The resistance and resistance-breaking mechanisms of pepper and counterpart CMV, respectively, remain to be investigated, which will enrich the genetic resources and accelerate CMV-resistant pepper breeding programs.
Park, Ji Eun,Kim, Mi-Ju,Lim, Myung Su,Kang, Sun Young,Kim, Jong Kwan,Oh, Seung-Hyeon,Her, Min,Cho, Yong-Hun,Sung, Yung-Eun Elsevier 2018 Applied Catalysis B Vol.237 No.-
<P><B>Abstract</B></P> <P>Graphitic carbon nitride-carbon nanofiber (g-CN-CNF) was synthesized as a bifunctional catalyst in an anion-exchange membrane water electrolyzer (AEMWE), and primary and rechargeable Zn–air cells. The g-CN-CNF catalyst shows high catalytic activity for oxygen reduction reaction and oxygen evolution reaction in half-cell, with low overpotentials and low Tafel slopes. The high activity is attributed to the synergistic effect of abundant active sites and the electrical conductivity following the pyrolysis of g-CN and CNF. As a result, AEMWE with the g-CN-CNF anode, the first application of a carbon-based catalyst, exhibits outstanding performance that is the highest record in the literature for AEMWE using a non-noble metal catalyst. In addition, the performance and durability of Zn-air cells with g-CN-CNF cathode outperform those fabricated with commercial platinum.</P> <P><B>Highlights</B></P> <P> <UL> <LI> Graphitic carbon nitride/carbon nanofiber composite (g-CN-CNF) is proposed as bifunctional catalyst for both ORR and OER. </LI> <LI> g-CN-CNF catalysts exhibited high activity toward oxygen evolution and reduction reactions. </LI> <LI> Anion exchange membrane water electrolyzer with g-CN-CNF showed high performance despite the application of the carbonaceous material. </LI> <LI> Rechargeable Zn-air battery also exhibited the high performance and capacity retention. </LI> </UL> </P> <P><B>Graphical abstract</B></P> <P>[DISPLAY OMISSION]</P>