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원발성 간세포암으로 오인된 위 간세포양 샘암종의 간 전이
문지윤 ( Ji Yoon Moon ),김광하 ( Gwang Ha Kim ),정재훈 ( Jae Hoon Cheong ),이봉은 ( Bong Eun Lee ),류동엽 ( Dong Yup Ryu ),송근암 ( Geun Am Song ) 대한소화기학회 2012 대한소화기학회지 Vol.60 No.4
Gastric hepatoid adenocarcinoma is a special type of gastric carcinoma, which produces AFP. We report a case of an metastatic gastric hepatoid adenocarcinoma mistaken for primary hepatocellular carcinoma (HCC). A 72 year-old woman was transferred to our hospital for treatment of the hepatic mass. She underwent subtotal gastrectomy for gastric cancer 2 years ago. A year ago, she was diagnosed with hepatic mass and treated with transhepatic chemoembolization under the suspicion of primary HCC in other hospital. The hepatic mass looked like primary HCC on CT, and serum AFP was elevated to 18,735 IU/mL. We did the transhepatic mass biopsy and compared it to the histology of the previous gastric cancer, The results of immunohistochemical staining between them was coincident, and so it was diagnosed as a hepatic metastasis of gastric hepatoid adenocarcinoma.
동반 심기형이 없는 수정 대혈관 전위 성인 환자에서 나타난 완전 방실 차단
한동철 ( Dong Cheul Han ),김준 ( Jun Kim ),문지윤 ( Ji Yoon Moon ),반지은 ( Ji Eun Ban ),이형두 ( Hyoung Doo Lee ),홍택종 ( Taek Jong Hong ),신영우 ( Yung Woo Shin ) 대한내과학회 2007 대한내과학회지 Vol.72 No.3
Patients with isolated congenitally corrected transposition of the great arteries (CCTGA) comprise 1% of all CCTGA patients. They are usually asymptomatic until functional abnormalities such as atrioventricular block or systemic atrioventricular valve regurgitation become complicated. We report here a case of a 33 year-old man with isolated CCTGA and complete AV block that underwent implantation of a permanent pacemaker using endocardial leads. During a 12 month follow-up period, no symptoms developed and lead-related parameters have been stable. (Korean J Med 72:311-314, 2007)
중증 전신홍반루푸스에서 Rituximab의 사용 경험 2예
황기원 ( Ki Won Hwang ),안용성 ( Yong Sung Ahn ),문지윤 ( Ji Yoon Moon ),김일영 ( Il Young Kim ),박영은 ( Young Eun Park ),김근태 ( Geun Tae Kim ),이준희 ( Jun Hee Lee ),김성일 ( Sung Il Kim ) 대한류마티스학회 2006 대한류마티스학회지 Vol.13 No.3
Rituximab is a chimeric monoclonal antibody for human B lymphocyte subset CD20 and has recently been used for treatment of autoimmune disease such as rheumatoid arthritis and systemic lupus erythematosus (SLE). We report the experiences of rituximab treatment in two patients with severe SLE. The first case is 16-year-old female patient with hemolytic anemia, thrombocytopenia and acute renal failure due to aggravation of lupus nephritis, and the second case is 30-year-old female pregnant patient with diffuse alveolar hemorrhage after preterm premature rupture of fetal membranes. All two patients responded to rituximab and maintained symptom free state.
선천적 등쪽 췌장 발육 부전증을 동반한 다비장 증후군 환자에서 나타난 급성 췌장염 와 내시경 초음파의 역할
정재훈 ( Jae Hoon Jeong ),김광하 ( Gwang Ha Kim ),송근암 ( Geun Am Song ),이동건 ( Dong Gun Lee ),문지윤 ( Ji Yoon Moon ),정재훈 ( Jae Hoon Cheong ),김석 ( Suk Kim ) 대한소화기학회 2012 대한소화기학회지 Vol.60 No.1
A 49-year-old female was admitted to our hospital for acute pancreatitis. The abdomen CT scan incidentally showed midline liver with hepatomegaly, centrally located gallbladder, pancreas truncation, right sided small bowel, left sided large bowel, interruption of the inferior vena cava with azygos continuation, preduodenal portal vein, and multiple spleens in the left upper quadrant. In MRCP, the head of pancreas was enlarged and short main pancreatic duct without accessory duct was showed. EUS revealed enlarged ventral pancreas with a main pancreatic duct of normal caliber, absence of the accessory pancreatic duct and the dorsal pancreas. She was diagnosed as polysplenia syndrome with agenesis of dorsal pancreas. It is a rare congenital anomaly frequently associated with various visceral anomalies including multiple spleens, impaired visceral lateralization, congenital heart diseases, gastrointestinal abnormalities and azygos continuation of the inferior vena cava. We report a case of polysplenia syndrome with agenesis of dorsal pancreas presenting acute pancreatitis. (Korean J Gastroenterol 2012;60:47-51)