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류마티스관절염에 동반된 ANCA 관련 불충분-면역성 사구체신염 2예
구본산 ( Bon San Koo ),김용길 ( Young Gil Kim ),최종기 ( Jong Gi Choi ),안용철 ( Yong Chul Ahn ),이성근 ( Seung Geun Lee ),이창근 ( Chang Keun Lee ),유빈 ( Bin Yoo ) 대한류마티스학회 2010 대한류마티스학회지 Vol.17 No.3
Renal involvement is one of the extra-articular manifestations found in patients with rheumatoid arthritis (RA). Membranous glomerulonephopathy, membranoproliferative glomeruonophritis, secondary amyloidosis, and focal segmental glomerulosclerosis are reported as pathologic diagnoses of renal involvement. However, reports of renal involvement in patients with RA and antineutrophil cytoplasmic autoantibody (ANCA)-associated pauci-immune glomerulonephritis are rare. Recently, we experienced two patients with RA who developed azotemia and were finally diagnosed with ANCA-associated pauci-immune glomerulonephritis. Because of the rarity of these cases, we report two cases in patients with RA with a literature review.
구본산 ( Bon San Koo ),송윤아 ( Yoonah Song ),이승훈 ( Seunghun Lee ),김태환 ( Tae-hwan Kim ),전재범 ( Jae-bum Jun ) 대한내과학회 2018 대한내과학회지 Vol.93 No.5
Systemic sclerosis (SSc) is a chronic autoimmune disorder characterized by endothelial and fibroblast dysfunction, resulting in progressive fibrosis of the skin and internal organs. Ankylosing spondylitis (AS) is an arthritic condition affecting the axial skeleton and peripheral joints. An association between SSc and AS is relatively rare, as the two diseases share few characteristics. Here, we present a case of limited SSc in a 44-year-old man who exhibited low-grade AS, and discuss several cases of coexisting SSc and AS in the literature. Patients with both diseases showed several common features, including male predominance, middle age, and combined interstitial lung disease. However, unlike our case, the patients reported in the literature had advanced ankylosis and diffuse SSc. (Korean J Med 2018;93:492-496)
담도 유두종증에 대한 광역동치료 후 실내 생활에서 발생한 광과민반응
박현우 ( Hyun Woo Park ),구본산 ( Bon San Koo ),배윤정 ( Yun Jeong Bae ),박도현 ( Do Hyun Park ),조유숙 ( You Sook Cho ),문희범 ( Hee Bom Moon ),김태범 ( Tae Bum Kim ) 대한내과학회 2010 대한내과학회지 Vol.79 No.1
Photodynamic therapy has been widely used in the treatment of various cancerous diseases. However, photodynamic therapy with a photosensitizer can cause a photosensitivity reaction on the skin. We report a case of a 64-year-old woman diagnosed with photosensitivity reaction after photodynamic therapy using the photosensitizer, porfimer. She presented to the emergency room with a skin rash on her face, neck, and both upper and lower extremities nine days after the photodynamic therapy. She denied any outdoor activity during that period. After administration of systemic corticosteroid and anti-histamine, her skin lesions resolved completely within seven days. (Korean J Med 79:92-95, 2010)
강세훈 ( Se Hun Kang ),이태훈 ( Tae Hoon Lee ),임현 ( Hyun Lim ),구본산 ( Bon San Koo ),이승범 ( Seung Bum Lee ),박영훈 ( Young Hoon Park ),나신 ( Shin Na ),박성준 ( Seong Joon Park ),나희경 ( Hee Kyong Na ),조유숙 ( You Sook Ch 대한천식알레르기학회 2011 천식 및 알레르기 Vol.31 No.1
Breast-feeding anaphylaxis is reported to be an extremely rare but potentially life-threatening condition. We report a 32-year-old woman who experienced recurrent anaphylaxis associated with breast-feeding. Generalized urticaria and angioedema accompanied by syncope were recurrent immediately after breast-feeding or milk letdown. Skin prick tests for the common food panel were all negative. UniCAP tests were performed to see if specific IgE to milk is present in her serum and the results was found to be negative. After weaning, the symptoms were completely resolved and never recurred. Based on her clinical course, it is believed that she had a breast-feeding anaphylaxis. (Korean J Asthma Allergy Clin Immunol 2011;31:55-58)