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신민경 ( Min Kyung Shin ),홍경국 ( Kyung Kook Hong ),유박린 ( Bark Lin Lew ),김낙인 ( Nack In Kim ) 대한피부과학회 2007 대한피부과학회지 Vol.45 No.12
Microscopic polyangiitis (MPA) is a systemic vasculitis that is histologically characterized by small vessel involvement. Although MPA is primarily associated with necrotizing and crescentric glomerulonephritis and pulmonary capillaritis, MPA often has cutaneous features. We report a case of microscopic polyangiitis with acral necrosis as the skin manifestation. A 56-year-old man presented with acral dry gangrene on tip of finger and toe and reticulated erythema on leg. He had suffered from proteinuria, hemoptysis, and arthralgia. Histopathologically, small vessel vasculitis without granuloma was seen. A high serum level of pANCA was detected by ELISA. This is a relatively rare disease, which has a poor prognosis in the absence of aggressive therapy, and is infrequently reported in dermatologic journals in Korea. (Korean J Dermatol 2007;45(12):1298∼1302)
Laugier-Hunziker 증후군에서의 구강 색소침착 병변에 대한 고찰
유박린 ( Bark Lynn Lew ),홍경국 ( Kyung Kook Hong ),이상길 ( Sang Kil Lee ),김효종 ( Hyo Jong Kim ),이무형 ( Mu Hyoung Lee ) 대한장연구학회 2005 Intestinal Research Vol.3 No.2
Oral pigmentation is seen fairly commonly in dermatologic practice. Oral pigmentation associated with Laugier-Hunziker syndrome (LHS) is an uncommon condition that shares some dermatologic features with Peutz-Jeghers syndrome (PJS). It is benign and asymptomatic, with no known cause, and is often associated with pigmentation of the nails and other mucosal surfaces. LHS and PJS show very similar skin manifestations but there age of onset, genetics, predilection site and associated systemic disease are different. However, evaluation of intestinal polyps should be performed for accurate differential diagnosis. We present seven patients whose conditions highlight the clinical syndrome known as LHS, and use the opportunity to review its clinical and pathologic features, and the relevant literature. (Intestinal Research 2005;3:145-149)