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Solitary Fibrous Tumor of the Urinary Bladder
김세훈,차경빈,최영득,조남훈 연세대학교의과대학 2004 Yonsei medical journal Vol.45 No.SUP
Solitary fibrous tumor (SFT) is a distinct spindle cell tumor arising mainly in the pleura, however, SFT of extra-pleural sites had been reported. To our knowledge, five cases of the urinary bladder SFT had been reported. We have recently experienced a case of SFT of the urinary bladder in a 56-year- old man who was admitted to the hospital with a 4-month history of voiding difficulty, frequency, and residual urine sensation. A computerized tomography scan revealed a 12cm sized intravesical mass. The mass was marginally excised under the impression of it being a benign spindle cell tumor by pre-operative needle biopsy. On gross examination, the mass was multinodular, creamy white, and the cut surface was fibrotic with a rubbery consistency. Microscopic examination revealed haphazardly arranged spindle cells with a lace-like deposition of inter- and pericellular collagen. Areas of increased cellularity show nuclear atypia and occasional mitoses (2-3/10HPF). The immunohistochemical staining revealed an intense CD34 and bcl-2 immunoreactivity. Although the exact biologic behavior of these tumors has not been clarified, most of the reported cases have undergone a benign clinical course.
김동석,차경빈,이승렬,김동준,조남훈,최영득 대한비뇨의학회 2004 Investigative and Clinical Urology Vol.45 No.4
A solitary fibrous tumor(SFT) is now commonly accepted to derive from mesenchymal cells differentiating toward fibroblast or myofibroblast. Although the extrapleural manifestations of SFT have been documented in almost all sites, an SFT arising in the genitourinary tract is extremely rare, with less than 10 cases having been reported. The histopathological criteria between a benign and a malignant SFT are obscure, and their biological behaviors remain controversial. The choice of treatment of an SFT remains to be clarifies. Herein, a case of a bladder SFT, well encased within the submucosa and bladder muscle, is reported. The SFT of bladder was completely excised, and there was no evidence of recurrence after 15 months of follow-up. (Korean J Urol 2004;45:393-395)