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조한별 ( Han Byoul Cho ),김재훈 ( Jae Hoon Kim ),홍순원 ( Soon Won Hong ),이현준 ( Hyun Joon Lee ),김민경 ( Min Kyoung Kim ),김성훈 ( Sung Hoon Kim ),김영태 ( Young Tae Kim ),김재욱 ( Jae Wook Kim ) 대한산부인과학회 2006 Obstetrics & Gynecology Science Vol.49 No.9
Uterine sarcomas are rare tumors of mesodermal origin and constitute 2-6% of uterine malignancies. They are classified into leiomyosarcoma (LMS), malignant mixed mullerian tumors (MMMTs), and endometrial stromal sarcoma (ESS) by histologic types. Endometrial stromal sarcomas account for about 7-15% of uterine sarcomas, about 0.2% of female genital tract malignancies. Endometrial stromal sarcomas are divided into endometrial stromal nodule, low-grade endometrial stromal sarcoma, and high-grade endometrial stromal sarcoma on the basis of mitotic activity and vascular invasion. Clinical outcome of low-grade endometrial sarcoma is better than that of high-grade endometrial stromal sarcoma and has a propensity for slow metastasis. We have experienced a case of low-grade endometrial stromal sarcoma with multiple metastasis in a 41-year-old woman and was treated by surgical resection and combination chemotherapy, which is presented with a review of brief literature.