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증예(症例) : 만성신부전 악화와 동반된 후천성혈우병 1예
정금모 ( Gum Mo Jung ),전성희 ( Sung Hee John ),김남돈 ( Nam Don Kim ),박용진 ( Yong Jin Park ),박요숙 ( Hyo Sook Park ) 전북대학교 의과학연구소 2003 全北醫大論文集 Vol.27 No.2
후천성혈우병은 매우 드문 질환으로 중증의 출혈이 흔하게 나타나고 이로 인한 사망률이 높기 때문에 조기에 정확히 진단하여 적절한 치료를 즉각적으로 시행하여야 한다. 저자들은 만성신부전증으로 치료중 지속적인 출혈로 인해 발견된 후천성혈우병 환자를 면역억제제를 사용하여 성공적으로 치료하고 이에 증례보고 하는 바이다. Acquired hemophilia due to factor Ⅷ inhibitor is a rare disease that occurs in about one per million people each year. In about 50% of patients the disorder is associated with other conditions, mainly the postpartum period, underlying malignancies, drug administration, or autoimmune disease, such as rheumatoid arthritis or systemic lupus erythematosus. It is associated with bleeding complications that can be life-threatening. However, these bleeding episodes can be controlled when the correct diagnosis is made quickly and appropriate therapy applied. We had a patient with acquired hemophilia who was presented with sustained bleeding during managing uremia. At first, the diagnosis was incorrect because of delayed inhibitor reactivity. But, by retestifying after 2 hour incubation of diluted plasma and assaying inhibitor titer, we could have correct diagnosis. And we successfully treated it with oral immunosuppressive agents.
2세대 약물 용출 관상동맥 스텐트 삽입 후 급성 심근 경색으로 병발한 관상동맥 연축 1예
김중근 ( Joong Keun Kim ),이신은 ( Shin Eun Lee ),박문식 ( Moon Sik Park ),윤소희 ( So Hee Yun ),이나은 ( Na Eun Lee ),이재운 ( Jae Un Lee ),이동엽 ( Dong Yub Lee ),박종필 ( Jong Pil Park ),전성희 ( Sung Hee John ),임지현 ( Ji Hyu 전북대학교 의과학연구소 2012 全北醫大論文集 Vol.36 No.1
Although several investigators have reported the coronary artery spasm after coronary artery stenting, all previous reports, coronary spasm after drug-eluting stent (DES) placement was occurred in first generation DES, such as sirolimus-eluting (Cypher®) and paclitaxel-eluting stents (Taxus®). Clinical relevance is unknown, the underlying mechanism may be delayed vascular healing due to toxic effects of the sirolimus and paclitaxel to endothelial cells (EC). The second-generation DES, such as everolimus-eluting (Xience V®) and zotarolimus-eluting stents (Endeavor®), are proving to be significantly more effective and safer than the first-generation DES.1)2) We report a patient with severe coronary artery spasm lead to myocardial infarction after second generation DES implantation at the site of detectable atherosclerotic lesion.