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박정엽(Jeong Youp Park),김유미(Yoo Mee Kim),강이화(Ea Wha Kang),김용수(Yong Soo Kim),심광용(Kwang Yong Shim),유내춘(Nae choon Yoo),강혜윤(Hae Youn Kang),박영년(Young Nyun Park),박찬일(Chan Il Park),노재경(Jae Kyung Roh) 대한내과학회 2001 대한내과학회지 Vol.61 No.2
Mucoepidermoid carcinoma is a common malignant tumor of the salivary glands, but rare in other sites. Only 10 cases of mucoepidermoid carcinoma of liver have been reported, and there was 1 case of double primary cancer of hepatocellular carcinoma and mucoepidermoid carcinoma. The definite diagnosis and pathogenesis are still controversial. However, hepatocellular carcinoma is the second most common cancer in Korea. Its etiology is better known compared to mucoepidermoid carcinoma. We report a rare case of double primary cancer of mucoepidermoid carcinoma and hepatocellular carcinoma in liver.(Korean J Med 61:162-167, 2001)
상안와열 증후군을 동반한 안와로 전이된 원발성 간세포암
박정엽(Jeong Youp Park),김유미(Yoo Mee Kim),심광용(Kwang Yong Shim),유내춘(Nae Choon You),노재경(Jae Kyung Roh) 대한내과학회 2001 대한내과학회지 Vol.60 No.2
The superior orbital fissure syndrome is a rare condition characterized by opthalmoplegia, ptosis, and proptosis of the eye, fixation and dilation of the pupil, and anesthesia of the upper eyelid and forehead. Tumor metastasis to the orbit is uncommon and there were only 11 histologically proven cases of metastatic hepatocellular carcinoma to the orbit. There was only one case of metastatic hepatocellular carcinoma to the orbit with superior orbital fissure syndrome. The prognosis were poor for all reported cases, but palliative radiotherapy could be some help. We report a rare case of metastatic hepatocellular carcinoma to the orbit with superior orbital fissure syndrome.(Korean J Med 60:179-182, 2001)
급성 전골수성 백혈병에 동반된 Wernicke disease 1 예
이상학(Sang Hak Lee),김현수(Hyun Soo Kim),서형찬(Hyung Chan Suh),이석(Seok Lee),정소영(So Young Chong),유내춘(Nae Choon Yoo),민유홍(Yoo Hong Min),한지숙(Jee Sook Hahn),고윤웅(Yun Woong Ko) 대한내과학회 1998 대한내과학회지 Vol.54 No.1
Wernicke`s disease is a condition produced by thiamine deficiency; more than 90% of the cases are observed in chronic alcoholics. Other less frequent conditions associated with Wernicke disease are gastric disorders, prolonged parenteral nutrition, uremia, hemodialysis, hyperemesis gravidarum, prolonged starvation, and AIDS. We report a 41-year-old female patient of Wernicke disease associated with nausea and prolonged parenteral nutrition after chemotherapy of acute promyelocytic leukemia. She has got thiamine replacement therapy and most symptoms were improved. She was discharged after complete remission of leukemia and recovery of normal diet.
결장암 환자에서 근치적 수술후 5 - Fluorouracil 과 lEUCOVORIN 보조 항암요법의 용량 미 용량 강도에 따른 효과
심광용(Kwang Yong Shim),안중배(Joong Bae Ahn),정희철(Hei Chul Jung),박준오(Joon Oh Park),유내춘(Nae Choon Yoo),라선영(Sun Young Rha),노재경(Jae Kyung Roh),김병수(Byung Soo Kim),김남규(Nam Kyu Kim),민진식(Jin Sik Min),정현철(Hyun Cheo 대한내과학회 2000 대한내과학회지 Vol.59 No.3
Background : In patients with stage C colon cancer, surgery followed by adjuvant chemotherapy with 5-fluorouracil (5-FU)/leucovorin (LV) is considered to be the standard treatment. However, the objects of adjuvant therapy and the duration of treatment are still matters of controversy. We investigated the effect of dose related factor(delivered total dose of 5-FU per body square meter, actual dose intensity and relative dose intensity) of the adjuvant 5-FU/leucovorin regimen on survival in coloncancer. Methods : Of the colon cancer patients with Duke's B2 and C stage diseases treated with curative resection from December, 1990 to December, 1996, 139 patients treated with 5-FU/LV as an adjuvant chemotherapy were evaluated. The delivered total dose of 5-FU per body square meter, actual dose intensity and relative dose intensity were obtained. The patients were divided into two groups according to the median value of each factor and the survival rates were compared. Results : The total dose of 5-FU administrated per body square meter had a significant effect on the 5-year disease free and overall survival in stage B2 and C colon cancer patients(B2; p=0.025, p=0.045, respectively, C; p=0.011, p=0.0002, respectively). But survival was not affected by the dose intensity. Multivariate analysis demonstrated that only the total dose of 5-FU administrated per body surface area affected the 5-year disease free and overall survival(p=0.0016, p=0.0007, respectively). Conclusion : It can be concluded that the total dose of 5-FU administered is more important than the DI in adjuvant chemotherapy of colon cancer and the total dose of 5-FU had a significant effect on the survival rate in colon cancer patients. To confirm the total dose effect of 5-FU on survival in this study, multi-institutional, prospective randomized studies should be carried out.(Korean J Med 59:290-299, 2000)
위암으로 전위절제술을 시행한 환자에서의 비타민 B12 결핍성 빈혈
고윤웅(Yun Woong Ko),민진식(Jin Sik Min),서형찬(Hyung Chan Suh),조준식(Joon Sik Cho),이석(Seok Lee),정소영(So Young Chong),유내춘(Nae Choon Yoo),민유홍(Yoo Hong Min),한지숙(Jee Sook Hahn) 대한내과학회 1998 대한내과학회지 Vol.54 No.3
Objectives: We attempt to find out the decremental character of serum vitamin B12 level and features of patients with vitamin B12 deficiency anemia occurring earlier than 4 years after total gastrectomy. Methods: We studied 91 patients who underwent total gastrectomy and select 59 patients who evaluate serum vitamin B12 level within 4 years after total gastrectomy to characterize the features of vitamin B12 deficiency anemia group occurring earlier than 4 years after the operation. Results: 1) In 91 patients, the mean postoperative duration is 31.9(range: 0-135) months and mean serum vitamin B12 level 158.9(total 159 times, range: 20.0-806.2) pg/mL. Correlation equation is y=403.30×e-0.09x +175.93×e-0.02x (r2=0.804). The postoperation duration that serum vitamin B12 level falls below 200pg/mL is 20 months. 2) Among 59 patient, there were 20 cases of vitamin B12 deficiency anemia group(Group I), 21 cases of vitamin B12 deficiency(Group II) and 39 cases of non-vitamin B12 deficiency group(Group III). Preoperation symptom duration in Group I was longer than that in Group II(18.2 vs 9.6 weeks, p<0.01). Group 1 and Group II showed lower serum vitamin B12 level than Group III(126.7 & 96.0pg/mL vs 330.4pg/mL, p<0.01). 3) Eleven cases had associated diseases(9 alcoholics and 2 liver cirrhosis) with vitamin B12 deficiency anemia and these disease had significant influence on the incidence of vitamin B12 deficiency anemia(p<0.01) within 4 years. Among the 30 cases who could measure iron profile, 10 patients had an iron deficiency anemia, There was a higher incidence of vitamin B12 deficiency anemia in iron deficiency anemia group(7/10, 70%) than that in non iron deficiency anemia group(7/20, 35%) but no statistical significance(p=0.12). 4) Although anti-cancer chemotherapy did not have a significant influence on the incidence of vitamin B12 deficiency anemia, vitamin B12 level in anti-cancer chemotherapy group was higher than that in non-chemotherapy group(201.83 vs 127.66pg/mL, p=0.01) at similar mean postoperation duration(27.8 vs 27.7 months, p=0.97). 5) The independent predictor of vitamin B12 deficiency anemia within 4 years were associated disease(p=0.002) and preoperation symptom duration(p=0.004), Conclusion: Red cell indices such as Hb or MCV did not have any clinical significances in predicting the development of vitamin Biz deficiency. To prevent vitamin B12 deficiency anemia and promote better quality of life in total gastrectomized patients with stomach cancer, careful monitoring of serum Vitamin B12 level and replacement therapy should be necessary at least 20 months after operation, especially in patients with associated disease and longer preoperation symptom duration.