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이한슬(Han Sul Lee),염상민(Sang Min Yum),이동채(Dong Chae Lee),김병훈(Byung Hoon Kim),이종효(Jong Hyo Lee),이승현(Sung Hyun Lee),김대식(Dae Sik Kim),김건형(Kun Hyung Kim),박순희(Soon Hee Park) 대한내과학회 2002 대한내과학회지 Vol.62 No.5
Allgrove syndrome, also known as Tripple A syndrome is characterized by ACTH-resistant adrenal insufficiency, achalasia of esophagus and alacrima. Since its first description by Allgrove et al. (1978), more than 60 cases from all over the world have been reported. In Korea, however, there was no report of this Allgrove syndrome. We report studies on a 18-year old male patient with this rare triad. The patient had alacrima from birth; isolated glucocorticoids deficiency had been diagnosed at 6 years of age and achalasia at age 18. We report the case with the review of literature.(Korean J Med 62:537-542, 2002)
이석 ( Seok Lee ),황호인 ( Ho In Hwang ),염상민 ( Sang Min Yum ),이완식 ( Wan Sik Lee ),박창환 ( Chang Hwan Park ),김현수 ( Hyun Soo Kim ),최성규 ( Sung Kyu Choi ),유종선 ( Jong Sun Rew ) 대한소화기학회 2008 대한소화기학회지 Vol.52 No.1
We present a case of intrapancreatic accessory splenic infarction in a 28-year-old woman. It was discovered during a workup for an acute right epigastric pain. Computed tomography imaging of abdomen demonstrated a hemorrhagic high attenuation with enhancing solid portion in the tail of pancreas. The clinical and radiological differential diagnosis included pancreatic mucinous cystic neoplasm, pancreatic endocrine neoplasm, solid pseudopapillary tumor, ductal adenocarcinoma, and metastasis. A distal pancreatectomy was completed. The microscopic examination revealed heterotopic splenic tissue with infarction and her abdominal pain disappeared. In this case report, we first describe a symptomatic accessory splenic infarction which presented as a hemorrhagic mass in the tail of pancreas mimicking pancreatic neoplasm. (Korean J Gastroenterol 2008;52:48-51)