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Marfan syndrome and symptomatic dural ectasia: A case report and literature review
엄시내,김광남,김동찬,김성혜 대한의학유전학회 2014 대한의학유전학회지 Vol.11 No.2
Dural ectasia refers to the widening or ballooning of the dural sac surrounding the spinal cord. It can affect any plane of thespinal canal, but occurs primarily in the lumbosacral region. Dural ectasia is present in 63-92% patients who have Marfansyndrome, and is related to Ehlers-Danlos syndrome, neurofibromatosis type I, and ankylosing spondylitis. The most commonsymptoms are low back pain, headache, weakness, numbness above and below the affected limb, and occasional rectaland genital pain. However, in most patients, dural ectasia is usually asymptomatic. We report the case of a 5-year-old boywho presented with a severe headache who had been diagnosed with Marfan syndrome. During the evaluation, magneticresonance imaging of the lumbar and sacral spine revealed dural ectasia. To our knowledge, this is the first report on Marfansyndrome with symptomatic dural ectasia in Korea. We concluded that dural ectasia should be suspected in patientsdiagnosed with Marfan syndrome who have a severe headache.
지압과 온열의 조합마사지가 인체의 스트레스 완화에 미치는 영향 평가
이대원,박지형,엄시내,김도원,조승현,고창용,김한성,Lee, Dae Won,Park, Ji Hyung,Eom, Si Nae,Kim, Do Won,Cho, Syung Hyun,Ko, Chang-Yong,Kim, Han Sung 대한의용생체공학회 2012 의공학회지 Vol.33 No.4
This study was designed to investigate the effect of a combined stimulus which was composed of chiropractic massage and thermotherapy on the relief of mental and physical stress. Fifteen healthy male subjects were treated with three type of stimuli; control (without any stimulus), a single stimulus (only chiropractic) and a combined stimulus. To evaluate the effects of stimuli, visual analogue scale (VAS), trunk extension, electromyogram (EMG) on erector spinae muscle and electrocardiogram (ECG) were measured and analyzed before and after stimuli. In the control group, there were no significant changes in EMG root mean square (RMS) value and low Frequency/high Frequency (LF/HF) ratio (p > 0.05, p > 0.05). However, both stimulus groups showed significant increases in trunk extension and EMG RMS values (p < 0.05, p < 0.05), but significant decreases in LF/HF ratios (p < 0.05). Particularly the decrement rate in LF/HF ratio was significantly higher in the combined stimulus group than that in the single stimulus group (p < 0.05). Also, a significantly lower VAS was recorded after combined stimulus. Our findings indicate that the combined stimulus might not only improve flexibility and strength of muscle, but also active parasympathetic nerve activity. The combined stimulus may thus contribute to relieve the stress and to enhance the muscle function.