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南仁鉉,李永來 전북대학교 의과학연구소 1981 全北醫大論文集 Vol.5 No.1
Omphalocele(Exomphalos) is a rare congenital anormaly which is a defect of the abdominal wall at the unbilicus with herniation of abdominal contents. The large lesion consists of the most abdominal visceras herniating into the base of the umbilical cord provides a covering of amniotic membrance and peritoneum. Gastroschisis differs from the omphalocele in that there is a normal insertion of the umbilical cord to the abdominal wall. Also there is paraumbilical full thickness abdominal wall defect and absence of sac covering the herniated viscera. We have experienced 2 patients of omphalocele including a case of ruptured comphalocele which is life threatening and reported with reviewed literatures at Department of Surgery, College of Medicine, Jeonbug National University.