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채동완 ( Dong Wan Chae ) 대한내과학회 2013 대한내과학회지 Vol.84 No.1
Recent change in major indication for renal biopsy from nephrotic syndrome to asymptomatic urinary abnormality (AU) in Korea makes IgA nephropathy the most common biopsy- confirmed glomerulonephritis (GN). Beside from the most common manifestation of AU, a significant portion (22%) of IgA nephropathy (IgAN) patient revealed the nephrotic-range proteinuria. About 1/3 of patients with minimal change disease (MCD), membranous nephropathy (MN) and focal segmental glomerulosclerosis (FSGS) presented with AU. In elderly patient (> 60 years), the proportion of cresentic glomerulonephritis, MN, and FSGS increased, while the prevalence of IgAN decreased compared to younger patients. MCD showed no change based on old age. GN was the third most common cause of ESRD constituting 11-15% of cases. ESRD patients from GN start dialysis younger and live longer on dialysis compared to diabetic and hypertensive patients in Korea. (Korean J Med 2013;84:1-5)
일반연제 발표 : 한국인에서 발생하는 IgA 신병증과 초점성 분절성 사구체 경화증에서 interleukin-10 promotor region의 유전적 다형성에 관한 연구
채동완 ( Chae Dong Wan ),김성균 ( Kim Seong Gyun ),오국환 ( O Gug Hwan ),윤종우 ( Yun Jong U ),구자룡 ( Gu Ja Lyong ),김근호 ( Kim Geun Ho ),노정우 ( No Jeong U ),임춘수 ( Im Chun Su ),김연수 ( Kim Yeon Su ),김성권 ( Kim Seong Gwo 대한신장학회 2002 춘계학술대회 초록집 Vol.21 No.1
독성 표피 괴사융해증과 동반된 급속 진행성 사구체신염 1 예
윤동석(Dong Seok Youn),구자룡(Ja Ryong Koo),김훈(Hoon Kim),김진철(Jin Chul Kim),김근호(Gheun Ho Kim),김형직(Hyung Jik Kim),채동완(Dong Wan Chae),전노원(Rho Won Chun),노정우(Jung Woo Noe),구대원(Dae Won Ku),최영희(Young Hee Choi),원남희 대한내과학회 1998 대한내과학회지 Vol.54 No.5
RPGN is a catastrophic form of acute glomerulone-phritis characterized by an abrupt onset and rapid deterioration of renal function resulting in o1iguria within weeks or months, BPGN is seen in a variety of systemic disorders, including systemic lupus erythematosus, poly arteritis nodosa, Wegener's granulomatosis and subacute bacterial endocarditis. In addition, RPGN is seen in association with a variety of primary renal diseases such as poststreptacoccal glomrulonephritis, merrkranoproli-ferative glomerulonephritis, and IgA nephropathy, Good-pasture's syndrome. Toxic epidermal necrolysis (TEN) is a drug induced life threatening disease characterized by extensive epidermal detachment, necrosis, and mucosal erosion. TEN may involve liver, lung, intestine, and kidney. But renal involvement has seldom been reported. We report on a 63-year-old patient who developed a RPGN with a TEN. Renal biopsy showed pauci-immune crescentric glomerulonephritis and skin biopsy showed edematous change with extravasated erytkvcytes in upper dermis and several individually necrotic keratinocytes. ANCA and FANA test was negative. Our patient recovered renal function with steroid pulse therapy. The pathophysiology of TEN is unresolved but abnormal cytokine release (e.g., tumor necrosis factor) has been implicated in pathogenesis of TEN. Because various cytokines have direct toxic effect on kidney structure, the tubular and glomerular damage may be related to the cytokines involved in TEN. To our knowledge, this is the first documenting the presence of RPGN in patients with TEN. And there maybe some relations between PRGN and TEN which require further study.