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Guana, Riccardo,Garofano, Salvatore,Teruzzi, Elisabetta,Vinardi, Simona,Carbonaro, Giulia,Cerrina, Alessia,Morra, Isabella,Montin, Davide,Mussa, Alessandro,Schleef, Jurgen The Korean Society of Pediatric Gastroenterology 2014 Pediatric gastroenterology, hepatology & nutrition Vol.17 No.4
Severe combined immunodeficiency (SCID) is a life-threatening syndrome of recurrent infections and gastro-intestinal alterations due to severe compromise of T cells and B cells. Clinically, most patients present symptoms before the age of 3 months and without intervention SCID usually results in severe infections and death by the age of 2 years. Its association with intestinal anomalies as multiple intestinal atresias (MIA) is rare and worsens the prognosis, resulting lethal. We describe the case of a four year-old boy with SCID-MIA. He presented at birth with meconium peritonitis, multiple ileal atresias and underwent several intestinal resections. A targeted Sanger sequencing revealed a homozygous 4-bp deletion ($c.313{\Delta}TATC$; p.Y105fs) in tetratricopeptide repeat domain 7A (TTC7A). He experienced surgical procedures including resection and stricturoplasty. Despite parenteral nutrition-associated liver disease, the patient is surviving at the time of writing the report. Precocious immune system assessment, scrutiny of TTC7A mutations and prompt surgical procedures are crucial in the management.
Riccardo Guanà,Salvatore Garofano,Elisabetta Teruzzi,Simona Vinardi,Giulia Carbonaro,Alessia Cerrina,Isabella Morra,Davide Montin,Alessandro Mussa,Jürgen Schleef 대한소아소화기영양학회 2014 Pediatric gastroenterology, hepatology & nutrition Vol.17 No.4
Severe combined immunodeficiency (SCID) is a life-threatening syndrome of recurrent infections and gastro-intestinal alterations due to severe compromise of T cells and B cells. Clinically, most patients present symptoms before the age of 3 months and without intervention SCID usually results in severe infections and death by the age of 2 years. Its association with intestinal anomalies as multiple intestinal atresias (MIA) is rare and worsens the prog-nosis, resulting lethal. We describe the case of a four year-old boy with SCID-MIA. He presented at birth with meco-nium peritonitis, multiple ileal atresias and underwent several intestinal resections. A targeted Sanger sequencing revealed a homozygous 4-bp deletion (c.313ΔTATC; p.Y105fs) in tetratricopeptide repeat domain 7A (TTC7A).He experienced surgical procedures including resection and stricturoplasty. Despite parenteral nutrition-associated liver disease, the patient is surviving at the time of writing the report. Precocious immune system assessment, scrutiny of TTC7A mutations and prompt surgical procedures are crucial in the management.
Riccardo Guanà,Salvatore Garofano,Elisabetta Teruzzi,Simona Vinardi,Giulia Carbonaro,Alessia Cerrina,Isabella Morra,Davide Montin,Alessandro Mussa,Jürgen Schleef 대한소아소화기영양학회 2015 Pediatric gastroenterology, hepatology & nutrition Vol.18 No.1
Severe combined immunodeficiency (SCID) is a life-threatening syndrome of recurrent infections and gastrointestinal alterations due to severe compromise of T cells and B cells. Clinically, most patients present symptoms before the age of 3 months and without intervention SCID usually results in severe infections and death by the age of 2 years. Its association with intestinal anomalies as multiple intestinal atresias (MIA) is rare and worsens the prognosis, resulting lethal. We describe the case of a four year-old boy with SCID-MIA. He presented at birth with meconium peritonitis, multiple ileal atresias and underwent several intestinal resections. A targeted Sanger sequencing revealed a homozygous 4-bp deletion (c.313ΔTATC; p.Y105fs) in tetratricopeptide repeat domain 7A (TTC7A). He experienced surgical procedures including resection and stricturoplasty. Despite parenteral nutrition-associated liver disease, the patient is surviving at the time of writing the report. Precocious immune system assessment, scrutiny of TTC7A mutations and prompt surgical procedures are crucial in the management.
A STAKEHOLDER APPROACH TO HERITAGE MARKETING STRATEGY
Angelo Riviezzo,Antonella Garofano,Maria Rosaria Napolitano 글로벌지식마케팅경영학회 2018 Global Marketing Conference Vol.2018 No.07
Despite the growing interest towards stakeholder marketing, research aimed at understanding how the marketing function may engage with the different company’s stakeholders (beyond the customers) for value creation is still scant. Therefore, new horizons need to be explored in search for research avenues and effective practices that may entrust a concrete role for stakeholders in marketing. Among the strategic assets that may be used to strengthen relationships with both internal and external stakeholders, corporate heritage emerges as potentially one of the most interesting. Indeed, scholars and practitioners have widely acknowledged the strategic value of heritage, a multifacets construct considered as a specific attribute of corporate identity able to connect past, present and future and inspiring solidity and credibility in different audiences. Thus, heritage has become the core of a specific marketing literature stream. However, the possibility of using corporate heritage (at strategic and operational level) to engage different stakeholders seems to have been little explored to date. This study aims at investigating corporate heritage as a vehicle of multi-stakeholder engagement, through an in-depth analysis of 20 long-lived Italian firms that stand out for the wise use of heritage marketing strategies. Specifically, we adopted an inductive approach to uncover the process of heritage marketing followed by the investigated companies. Thus, the study helps to interpret and deepen the role of corporate heritage as a platform for stakeholder engagement, according to an integrated, strategic and multi-stakeholder perspective that has been to a large extent neglected by previous literature; furthermore, it presents an ideal decomposition of the strategic process of heritage marketing in key stages, with a precise indication of the stakeholder engagement opportunities referred to each stage; finally, it presents a categorization of the main tools and activities that companies may use to convey their historical and cultural heritage to the different stakeholders, both in and out of the business domain.