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양안 수직근육전이술로 치유된 양안 듀안안구후퇴증후군 1예
조윤애,오인경,Yoonae A,Cho,In Kyung Oh 대한안과학회 2006 대한안과학회지 Vol.47 No.6
Purpose: To report a male infant with bilateral Duane`s retraction syndrome treated with bilateral horizontal transpositions of vertical recti to the lateral rectus muscle. Methods: An 8-month-old boy showed bilateral Duane`s retraction syndrome with esotropia of 45PD, severe limitation of abduction (-4 and -3.5 in each eye) and mild globe retraction in both eyes. It was assumed that he inherited the condition from his father through an autosomal dominant pattern. His father showed esotropia of 25PD with -4 limitation of abduction in the left eye and a left head-turn of 10。. He also had +2 globe retraction, +1 upshoot and +2 downshoot in adduction of the left eye. Transposition of two vertical recti to the lateral rectus muscle was performed in both eyes of the boy. Results: Nine months after surgery, the boy had achieved a microesotropia of 6PD in primary gaze with stereopsis of 3000 seconds of arc and considerable improvement in abduction (-2, -1.5 in each eye). The amount of correction of esodeviation was 39PD. This favorable state was maintained at follow-up 3.5 years after surgery. Conclusions: An 8-month-old boy who had esotropia of 45PD caused by bilateral Duane`s retraction syndrome, underwent bilateral horizontal transpositions of vertical recti to the lateral rectus muscle. He achieved a microesotropia of 6PD in primary gaze and considerable improvement of abduction with only mild eyeball retraction.
선천 상사근 결손 환아의 하사근 비측 전치술 치료 1예
박진환,차덕선,조윤애,서영우,Jin-hwan Park,MD,Deoksun Cha,MD,Yoonae A,Cho,MD,PhD,Young-Woo Suh,MD,PhD 대한안과학회 2010 대한안과학회지 Vol.51 No.7
Purpose: To report a patient with absence of the superior oblique (SO) muscle of the left eye, who showed improvement after anterior and nasal transposition of the inferior oblique muscle for left hyperdeviation and right head tilt. Case summary: A two-year-old boy presented with hypertropia of the left eye and right head tilt. Alternate prism-cover test in the primary position demonstrated 18 prism diopters (PD) of left hypertropia, which increased to 35 PD in the left head tilt position. A version test demonstrated overaction of the left inferior oblique muscle and underaction of the left superior oblique muscle. As an orbit CT scan showed absence of the SO muscle, the patient was diagnosed with congenital absence of SO and left anterior and nasal transposition of the inferior oblique muscle was performed. Three weeks after surgery, the patient presented with orthotropia at distant and near. The version test revealed normal oblique muscles. There was no vertical deviation shown on the Bielschowsky head tilt test. The abnormal head posturing was no longer observed. Conclusions: The authorsreport a patient manifesting abnormal head posture and hypertropia, diagnosed with absence of SO muscle, which was successfully corrected using anterior and nasal transposition of the inferior oblique muscle.