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정희영(Hee-Young Cheong),윤희철(Hee-Chul Yoon),서은숙(Eun-Sook Suh) 대한소아신경학회 2004 대한소아신경학회지 Vol.12 No.2
저자들은 생후 19개월 환아에서 우측 편마비로 내원하여 뇌기저핵 경색이 있었던 환아에서 전신성홍반성 루프스와 관련됨을 발견하여 문헌 고찰과 함께 보고하는 바이다. Systemic lupus erythematosus(SLE), a rheumatic disease of unknown causes, is characterized by autoantibodies directed against self-antigens, resulting in inflammatory damages to target organs including kidney, blood-forming cells, and central nervous system. The prevalence rates are higher in Native Americans, Asians, Latin Americans and black people. A female to male ratio of approximately 2 : 1 occurs before puberty, and 4 : 1 after puberty. Children of SLE most frequently present with fever, fatigue, arthralgia or arthritis, and rashes. The diagnosis is confirmed by clinical and also laboratory manifestations satisfying at least 4 out of 11 criteria. A central nervous system is not rarely involved in children of SLE with the prevalence rate of 23-44%. However, cerebral infarcts are not a common phenomenon and can be seen only for 6% of children with SLE. There have been no cases reported in Korea. This is why we present a case of basal ganglia infarct associated with SLE in a 19-month old girl. We report this case with a brief review of related literature.