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Von Willebrand factor 이상을 보이는 Heyde 증후군
이태영 ( Lee Tae Yeong ),한상영 ( Han Sang Yeong ),문성훈 ( Mun Seong Hun ),장채령 ( Jang Chae Lyeong ),장진석 ( Jang Jin Seog ),박미경 ( Park Mi Gyeong ),이종훈 ( Lee Jong Hun ),노명환 ( No Myeong Hwan ),신우원 ( Sin U Won ),최 대한소화기학회 2004 대한소화기학회지 Vol.43 No.2
A 68-year-old woman with known severe aortic stenosis was admitted to the hospital because of hematochezia and dizziness. She had received several blood transfusions over the preceding 3 years and undergone right hemicolectomy 2 years ago for severe lower gastrointestinal bleeding. Postoperative histology revealed angiodysplasia involving the ascending colon. After the hemicolectomy, she continued to have hematochezia and anemia and required additional blood transfusions for anemia. During this admission, platelet count, activated partial- thromboplastin time, von Willebrand factor antigen, and von Willebrand factor ristocetin cofactor were normal. She had a severe deficiency of high-molecular-weight multimers of von Willebrand factor. Colonoscopy showed angiodysplasia in the transverse colon at this time. Successful coagulation of the bleeding angiodysplasia was achieved by argon plasma coagulator. No additional bleeding was observed thereafter. We report a case of Heyde`s syndrome with abnormal von Willebrand factor in a patient who presented with intestinal angiodysplasia and aortic stenosis. (Korean J Gastroenterol 2004; 43:133-136)