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혀와 손발의 레이노 현상으로 발현된 소아기 혼합결합조직병 1예
정순명 ( Soon Myung Jung ),유진택 ( Jin Taek Yoo ),김영환 ( Young Hwan Kim ),서유나 ( Yu Na Seo ),이나영 ( Na Young Lee ),이승근 ( Seong Geun Lee ),박성후 ( Seong Hu Park ),박영은 ( Young Eun Park ),백승훈 ( Seung Hoon Baek ),김 대한류마티스학회 2012 대한류마티스학회지 Vol.19 No.6
Mixed connective tissue disease (MCTD) was first described by Sharp and coworkers in 1972, characterized by symptoms of Raynaud`s phenomenon or swollen hands, overlapping clinical features of systemic lupus erythematosus, systemic sclerosis, or polymyositis/dermatomyositis, and the presence of anti-U1 RNP antibody. MCTD is rare in children and constitutes 0.3∼0.6% of all rheumatologic patients in pediatric rheumatology database of the United States. Here, we report the first Korean case of a 10-year-old female patient with MCTD, presenting Raynaud`s phenomenon in the hands, feet, and tongue.
반복되는 복통으로 진단된 호산구성 위장관염에 동반된 호산구성 복수와 방광염 1예
이순일,박희승,하병길,김동현,유진택,최성호 고신대학교 의과대학 2011 고신대학교 의과대학 학술지 Vol.26 No.2
Eosinophilic gastroenteritis is a relatively uncommondisease of unknown etiology and pathogensis. It is characterized by massive tissue eosinophilia, that can involve any layers of the gastrointestinal tract wall. The gastrointestinal signs and symptoms usually reflect the layer which is most severly affected. Eosinophilic gastroenteritis can be rarely accompanied by extraintestinal involvement. We report a case of a 19-year-old male with repeated epigastric and low abdominal pain. An abdominal computed tomography showed diffused wall thickeningof esophagus, small bowel and bladder with ascites. Esosinophilic infiltration was shown by multiple biopsies of the esophagus, duodenum on esophagogastroduodenoscopy and peritoneal fluid analysis. The patient was diagnosed with eosinophilic gastroenteritis, accompanied by esosinophilic ascites and cystitis and was treated with corticosteroid and ketotifen. Abdominal pain was improved dramatically.