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류마티스 : 원발성 쇼그렌 증후군에서 발생한 다발성 경화증 1예
황주희 ( Joo Hee Hwang ),이원석 ( Won Seok Lee ),최윤정 ( Yun Jung Choi ),오유정 ( Yoo Jeong Oh ),강미희 ( Mi Hee Kang ),류완희 ( Wan Hee Yoo ) 대한내과학회 2015 대한내과학회지 Vol.89 No.6
Sjogren syndrome (SS) is a chronic inflammatory autoimmune disorder involving the exocrine glands, which often presents with salivary and tear gland dysfunction leading to dry mouth and eyes (sicca symptoms). This disease occurs alone as primary SS, or in the background of connective tissue diseases as secondary SS. Neurological involvement is seen in 20-25% of SS cases. Cerebral involvement is generally heterogeneous both in terms of localization (focal or diffuse) and progression (acute, progressive or reversible) and may resemble the clinical and radiological findings of multiple sclerosis (MS). Here we present the case of a patient with primary SS who experienced acute progressive diffuse MS. (Korean J Med 2015;89:733-737)
류마티스 : 미만성 폐포출혈증후군으로 발생한 척-스트라우스 증후군의 1예
강미희 ( Mi Hee Kang ),이원석 ( Won Seok Lee ),최윤정 ( Yun Jung Choi ),오유정 ( Yoo Jeong Oh ),황주희 ( Joo Hee Hwang ),류완희 ( Wan Hee Yoo ) 대한내과학회 2015 대한내과학회지 Vol.89 No.6
Churg-Strauss syndrome (CSS), known as eosinophilic granulomatosis with polyangiitis, is a rare type of systemic vasculitis characterized by the presence of asthma, peripheral eosinophilia, and necrotizing vasculitis with eosinophilic infiltration of multiple organs. Approximately 3-4% of all CSS cases are associated with alveolar hemorrhage. Untreated CSS may lead to a poor prognosis, but glucocorticoid and cytotoxic agent treatments may result in clinical remission. The careful diagnosis and understanding of CSS is important for making treatment decisions and providing effective care. Here, we report a case of CSS with diffuse alveolar hemorrhage. (Korean J Med 2015;89:738-741)