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하시모토 갑상선염에서 갑상선 유두암과 여포암이 동시 발견된
홍진헌 ( Jin Hon Hong ),남수민 ( Soo Min Nam ),이미영 ( Mi Young Lee ),고장현 ( Jang Hyun Koh ),신장열 ( Jang Yeol Shin ),정춘희 ( Choon Hee Chung ),조미연 ( Mee Yon Cho ) 대한내과학회 2007 대한내과학회지 Vol.72 No.5
We report here on a rare case of papillary and follicular carcinoma of the thyroid gland that developed in a 31 years old woman who was previously diagnosed with Hashimoto`s thyroiditis. Her chief complaint was a palpable neck mass. The antimicrosomal and antithyroglobulin antibody levels were elevated. Ultrasonography of the left thyroid gland revealed a 2.5×2.0 cm sized thyroid nodule. Fine needle aspiration biopsy of the thyroid nodule was done and this was diagnosed as Hashimoto`s thyroiditis. There was no evidence of thyroid cancer. After 1 year, thyroid ultrasonography and biopsy were repeated for examining an enlarged thyroid nodule. Total thyroidectomy was then performed. The histopathologic examination revealed that the right and left thyroid glands were in accordance with the diagnosis of papillary and follicular cancer, respectively. Until now, no known case of simultaneous papillary and follicular carcinoma in Hashimoto`s thyroiditis has been reported. This case suggests that adequate follow up for Hashimoto`s thyroiditis patients with thyroid nodule may help the early detection and management of thyroid cancer. (Korean J Med 72:558-562, 2007)
양측성 비폐쇄성 수신증 및 중추성 요붕증을 유발한 중격-시신경 형성장애
김종현 ( Jong Hyun Kim ),이광복 ( Kwang Bok Lee ),이정훈 ( Jeong Hun Lee ),남수민 ( Soo Min Nam ),이강우 ( Kang Woo Lee ),황유진 ( Eu Gene Hwang ),길건 ( Geon Gil ) 대한내과학회 2014 대한내과학회지 Vol.87 No.2
A 27-year-old male with nonobstructive hydronephrosis was referred from the urology department for polyuria evaluation and management. The patient was hospitalized for urinary tract infection and cystostomy was performed due to neurogenic bladder of unknown origin. The patient was of short stature and had visual impairment. From the interview, we discovered he had been suffering from polyuria and polydipsia for more than 20 years. Urine output was 13 L/day and urine osmolarity was 85 mOsm/kg. The results of a water deprivation test were consistent with central diabetes insipidus. Septo-optic dysplasia (SOD) was observed on brain magnetic resonance imaging (MRI). SOD is a very rare condition characterized by agenesis of the septum pellucidum or corpus callosum, which may cause optic nerve aplasia or hypoplasia, midbrain abnormalities and/or hypopituitarism. After desmopressin treatment, polyuria and hydronephrosis were improved. We report a case of a 27-year-old male diagnosed with SOD including diabetes insipidus, resulting in nonobstructive hydronephrosis. (Korean J Med 2014;87:209-214)
그레이브스병과 동반된 자가면역성 갑상선 질환 관련 뇌병증 1예
박경선 ( Kyoung Sun Park ),이신희 ( Shin Hee Lee ),조남열 ( Nam Yeol Cho ),최유아 ( Yu Ah Choi ),고윤명 ( Yun Myoung Ko ),남선우 ( Seon Woo Nam ),남수민 ( Soo Min Nam ) 대한내과학회 2016 대한내과학회지 Vol.91 No.2
A patient with encephalopathy associated with autoimmune thyroid disease (EAATD), which is one of the most important differential diagnoses of treatable dementia, presents with various neurological symptoms, such as repetitive epileptic seizures, altered mental status, and cognitive dysfunction. Steroid treatment is effective for EAATD. The incidence of EAATD increases considerably with age, particularly in female patients. Most patients with EAATD have normal thyroid function test results or mild hypothyroidism. Patients with EAATD with Graves’ disease are very rarely reported. Here, we report a case of a 63-year-old woman who complained of declining cognitive ability and ataxia. She was diagnosed with EAATD accompanied by Graves’ disease. Her neurological symptoms improved after intravenous steroid administration. (Korean J Med 2016;91:197-201)