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이형접합제 PiMZ 및 α1 - Antitrypsin 결핍을 보인 간경변증
기춘석(Choon Suhk Kee),박경남(Kyung Nam Park),이민호(Min Ho Lee),안명주(Myung Ju Ahn),고윤석(Youn Suck Koh),함준수(Joon Soo Ham),이종철(Song Chul Lee),강종명(Jong Myung Kang) 대한소화기학회 1987 대한소화기학회지 Vol.19 No.1
In 1969, Sharp described the first cases of aplhai-antitrypsin deficiency disease in children with juvenile liver cirrhosis. Since then, this inborn error has been recognized as one of the more common factors in cirrhosis of infancy and childhood, especially in Caucasians of Northern Europeans. PiZZ phenotype is the only one associated with liver disease, there have been a few rescent reports of cirrhosis in heterozygous patients. We experienced a case of 24-year-old male patient who was diagnosed as liver cirrhosis by biopsy but had no defintie causes of liver cirrhosis. The laboratory findings were compatible with liver cirrhosis. By biopsy, the liver is composed of variable sized, micro and macronodules. Dense fibrous tissue encase these nodules. The hepatocytes are strongly positive granules and diastase resistant. Pi phenotype was Pi MIZ by IEF (immunoelectric Focusing) method and the plasma alphai- antitrypsin level is lower than normal.
B 형 간염바이러스와 연관된 각종 간질환군에서의 혈중 Alphal - Antitrypsin 치의 의의
고윤석(Youn Suck Koh),류우진(Woo Jin Lew),윤호주(Ho Ju Yun),함준수(Joon Soo Hahm),이종철(Jong Chul Rhee),이민호(Min Ho Lee),기춘석(Choon Suhk Kee),박경남(Kyung Nam Park) 대한내과학회 1988 대한내과학회지 Vol.35 No.1
N/A We studied the clinical significance the progress of of α1-antitrypsin (a-AT) as an indicator of hepatitis B virus related diseases, and as a marker of hepatoma by estimating the serum α1-AT level. The results are as follows: 1) The mean and standard deviation of the serum α1-AT level in each group was 198+30 mg/dl in healthy controls, 174±29mg/dl in healthy carriers, 263±68mg/ dl in acute viral hepatitis, 203±57 mg/dl in chronic viral hepatitis, 233±50mg/dl in chronic active hepatitis, 237±71mg/dl in liver cirrhosis, and 346±101mg/dl in hepatoma. 2) The α1-AT level of hepatoma showed the highest elevation in each group (p<0.05). 3) When using 330mg/dl of a-AT as the cut-off value of hepatoma, 27 of 52cases of hepatoma were included. In 20cases of hepatoma which were below 500ng/ml of alpha-Fetoprotein, 12 of the cases were above 330mg/dl of α1-AT. 4) When considering the convenience and laboratory cast of α1-AT, with the above results, we suggest that more extensive studies be done, in the areas of α1-AT as an indicator of the progress of hepatitis B virus related diseases, and as a complemental marker of hepatoma.
원발성 간암환자에서 간동맥 색전술의 치료효과 - 2. 중간 추적 생존율 -
고윤석(Youn Suck Koh),노임환(Im Hwan Roe),안정경(Jung Kyung Ahn),함준수(Joon Soo Hanm),이민호(Min Ho Lee),기춘석(Choon Suhk Kee),박경남(Kyung Nam Park),이은희(Eun Hee Lee),서흥석(Heung Suk Seo) 대한내과학회 1988 대한내과학회지 Vol.35 No.3
N/A Currently, primary hepatocellular carcinoma (HCC) is the second most common cause of cancer death in men in Korea. Generally, the tumor is unresectable due to underlying liver cirrhosis. As a palliative therapy of HCC, transcatheter arterial embolization (TAE) was performed in 53 patients (57 times) from April 19S5 until December 1986 at Hanyang University hospital, of which the conditions of only 35 patients could be followed after TAE therapy. We have analyzed the effectiveness of TAE therapy on these 35 patients. The results were as follows: In patient who didn't have tumor thrombosis in the first or second portal branches, the mean 8 months survival was 58.2%, while in patients with tumor thrombosis, it was 8.3%. The ratio of the tumor size to the liver measured by a planimeter in hepatic angiography was found to be meaningful in the prognosis; In patients with a ratio below 20%, the 6 months survival rate was 66.7%, and in patients with a ratio of 20% or more, it wis 43.4%, The results suggest that TAE is more beneficial in unresectable HCC which doesn't have tumor thrombosis in the first or second portal branches, and which has a ratio of tumor size to liver below 20% as measured by angiography.
간장및 담도 : 담석 핵화에 있어서의 단백질의 의의에 관한 연구
함준수(Joon Soo Hahm),기춘석(Choon Suhk Kee),박경남(Kyung Nam Park),이민호(Min Ho Lee),이종철(Jong Chul Lee),한동수(dong Soo Han),양석철(Suck Chul Yang),이광수(Kwang Soo Lee) 대한소화기학회 1990 대한소화기학회지 Vol.22 No.2
N/A Formation of gallstones depends upon at least 2 processes; first, supersaturation of cholesterol and calcium salts, seond, nucleation of crystals in the bile. Nucleation requires gallbladder mucins, and its main component, glycoprotein, is known to be concentrated in the gallstones. Howere the nature and role of the gallstone proteins is still unknown, and the difference in the compositions of proteins between various gallstones has not been observed. 21 gallstones, 13 cholesterol stones and 8 pigment stones, were obstanined at cholecystectomy, washed, dried and extracted cholesterol, pigment, and bile salts by 0.1 N HCl petrolium ether ethanol solution for an analysis of proteins in gallstones. The compositions of gallstones by infrared sphectophmeter. The gallstone proteins were then quantified by Bensadoun & Weinstein method, and analyzed by SDS-polyacrylamide gel eletrophoresis. The results were as follaws; 1) The amount of gallstones proteins was 2.12 mg% in cholesterol stones and 2.61mg% in pigment stones. 2) SDS-PAGE could isolate low molecular proteins; 13 cases (62%) below 15 KD, 3 cases (14.2%) between 20~40 KD and 5 cases (23.8%) above 45 KD of molecular weight. 3) There was no significant difference in protein quantification between cholesterol and pigment stones. We could suggest that gallstone proteins are mainly acidic proteins with low molecular weight and these proteins could play an important role in nucleation of gallstone formation.
Digitalis 투여후 폐경기환자의 질점막 도말검사에서 나타난 Estrogen 양 효과
정준호 ( Joon Ho Chung ),기춘석 ( Choon Suhk Kee ),최영길 ( Yong Kil Choi ),우대석 ( Dae Suck Woo ),정구명 ( Koo Myung Chung ) 대한내과학회 1971 대한내과학회지 Vol.14 No.12
Digitalis has been known to posses an estrogen like activity documented by gynecomastia and suppression of urinary gonadotrophin excretion. A study was designed to observe the digitalis effect on atrophic vaginal cells in 16 postmenopausal woman and a pati
간장 ( 肝臟 ) 및 담도 ( 膽道 ) : 만성 간염 환자에 있어서의 Ursodeoxycholic Acid ( SGD - FR ) 의 임상 효과
함준수(Joon Soo Hahm),이동후(Dong Hoo Lee),기춘석(Choon Suhk Kee),박경남(Kyung Nam Park),양석철(Suck Chul Yang),김태환(Tae Hwan Kim),이종철(Chong Chul Lee) 대한소화기학회 1990 대한소화기학회지 Vol.22 No.4
N/A Randomized double blind trials have done to determine the effect of ursodeoxycholic acid (SGD-F) to the progress of the chronic hepatitis, 30 patients who had been admitted at the department of internal medicine, Hanyang University Hospital from October 1989 to March 1990 were selected to the study; UDCA was given to 15 patients and placebo was given to the other 15 patients. The results are as follows; 1) Clinical stage showed improvement (14 cases; 93.3%) and serum transaminase was decreased markedly after UDCA (SGD-F) treatment. 2) Serum transaminase (SGOT, SGPT) was more decreased in UDCA treatment group than in placebo treatmelnt group. 3) The UCDA (SGD-F) treatment group showed more clinical improvement than the placebo treatment group. In conclusion, the ursodeoxycholic acid (SGD-F) treatment may be effective for patients with chronic liver disease.
이규택(Kyu Taek Lee),성건형(Keon Hyung Sung),양석철(Suck Chul Yang),이오영(Oh Young Lee),이종철(Jong Chul Rhee),함준수(Joon Soo Hahm),이동후(Dong Hoo Lee),기춘석(Choon Suck Kee),박경남(Kyung Nam Park) 대한내과학회 1991 대한내과학회지 Vol.40 No.6
Clinical observations made on 970 patients with lower gastrointestinal bleeding (hematochezia) admitted to Hanyang Universtiy Hospital over a period of 7 years starting from January 1983, revealed the following results. During the study period, patients with lower GI bleeding comprised 1.6% of the total numbers of patients admitted to the Depatment of Internal Medicine and General surgery, and the annual distribution of the patients remained unchanged. Casses of 970 patients with lower gastrointerstinal bleeding were hemorrhoid and anal fissure in 65.5%, malignant neoplasm in 21.1% (rectal cancer 16.9%, sigmoid cancer 3.3%, and anal cancer 0.9%), benign neoplasm in 4.0%, ulcerative colitis in 3.3%, acute infectious colitis in 1.9%, ischemic colitis in 1.7%, radiation colitis in 1.3% diverticulosis in 0.3%, and miscellaneous in 0.1%. The annual incidences of ulcerative colitis and recto-sigmoid cancer increased but that of infectious colitis decreased and others remained unchanged. There was no overall sexual difference. The peak age for hemorrhoid and anal fissure were 30's, benign neoplastic polyps and ulcerative colits were the 40's, malignant neoplasm was the 50's, and radiation and ischemic colitis were the 60's. Patients who required transfusion were 10.8%. Patients with ulcerative colitis (21.9%) and radiation colitis (23.1%) required more transfusions. Patients who improved with conservative treatment only wre 20.2%, and 79.8% required surgical intervention. In the management of benign neoplastic polyps, 51. 2% was treated with ploypectomy.
함준수(Joon Soo Hahm),이동후(Dong Hoo Lee),기춘석(Choon Suhk Kee),박경남(Kyung Nam Park),이민호(Min Ho Lee),이종철(Jong Chul Lee),양석철(Suck Chul Yang),김병연(Byung Yeun Kim),최태열(Tea Yeal Choi) 대한소화기학회 1991 대한소화기학회지 Vol.23 No.1
N/A Alpha 1-antitrypsin (AAT) is the most abundant circulating inhibitor of proteolysis and is responsible for most of the inhibition of trypsin by blood plasma. The AAT has been considered in searching for a new biochemical tumor marker in the diagnosis of malignant diseases. We estimated the level of AAT in serum of control (18) and patients with hepatoma (22), other malignant diseases (22), chronic liver diseases (25), and acute infectious diseases (10) by radial immunodiffusion (RID) in order to study the clinical significance of AAT as a marker of malignancy, especially hepatoma. The results were as follows; 1) The levels of AAT in normal control serum were 191 +- 46 mg/dL 2) The levels of AAT in patients with hepatoma and other malignant diseases (stomach cancer, lung cancer, colon cancer, pancreatic cancer, prostate cancer, and malignant lymphoma) were 331 +- 110 mg/dL and 285 +-112 mg/dL, respectively. A significant correlation between each groups was not observed (p>0.05). And the serum AAT levels were significantly higher in patients with malignant diseases than in normal controls (p<0.05). 3) The levels of AAT in chronic liver diseases (chronic hepatitis, and liver cirrhosis) were 229 +- 84 mg/dL and were not significntly higher than those of normal control (p>0.05). 4) The levels of AAT in acute infectious diseases (enteric fever, lung abscess, pneumonia and FUO) were 287 +- Slmg/dL.
간장 ( 肝腸 ) 및 담도 ( 膽道 ) : 울혈성 위질환 ( Congestive Gastropathy ) 과 만성간질환의 상관관계에 대한 연구 - 표식자로서의 의의 -
함준수(Joon Soo Hahm),이동후(Dong Hoo Lee),이민호(Min Ho Lee),이종철(Jong Chul Rhee),기춘석(Choon Suck Kee),안종훈(Jong Hoon Ahn),박경남(Kung Nam Park),박병권(Byung Kwon Park) 대한소화기학회 1990 대한소화기학회지 Vol.22 No.3
N/A The fact that gastric mucosal lesions are frequently seen in portal hypertension is already well known. In recent years, many workers reported that endoscopic features of gastric mucosa with portal hypertension showed minimal inflammation and marked venous ectasia and dilatation. However, the pathogenesis and pathophysiology and the diagnostic value of portal hypertension of these changes have been argued by many authors. Our purpose of the study is concerned about the incidence and the significance of congestive gastropathy on various chronic liver disease. For this aims, First, retrospectively the results of endoscopic features and liver biopsies of the 477 patients with abnormal liver function test were analyzed, investigated the incidence of these changes, and Second, prospectively selected 10 patients with normal liver function test and congestive gastropathy on the proximal part of the stomach, and unresponsive to anti-erosive medication, were under taken liver biopsies. The result was as follows; 1) The incidence of congestive gastropathy was similar in liver cirrhosts and in other types of chronic liver disease (p<0.05). LC 20.3% (38/187), CAH 16.8% (21/125), CPH 15.5%, (9/58), and others 14.3% (12/84). 2) In second study, 7 of the 10 patients undertaken liver biopsy probed to be the chronic liver diseases. 3) The liver function test of the one of the two who had no pathology on liver biopsy to be abnermal during follow-up 4 month in second study. These suggested that congestive gastropathy was found on various chronic liver disease and the possible stigmata even if without any other sign of the chronic liver disease.