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허재혁 ( Jae Hyuk Heo ),최은정 ( Eun Jeong Choi ),유승정 ( Seung Jung Yu ),박요한 ( Yo Han Park ),최정식 ( Jung Sik Choi ) 대한소화기학회 2022 대한소화기학회지 Vol.79 No.2
Neuroendocrine tumors (NETs) that arise from neuroendocrine cells can develop in most organs; however, it is rarely found in the duodenal papilla. Conversely, gastrointestinal stromal tumors (GISTs), which are mostly asymptomatic and detected incidentally, are usually found in the stomach and very rarely occur metachronously with NETs. A 42-year-old female with no specific underlying disease underwent gastroscopy due to epigastric pain. Biopsy of enlarged major and minor duodenal papilla confirmed the diagnosis of a NET. Endoscopic papillectomy of the major and minor papillae was performed. Multiple duodenal and jejunal submucosal nodules were seen on biliary CT performed at the 30 months follow-up. Pylorus-preserving pancreaticoduodenectomy was performed due to the suspicion of multiple recurrent NETs and muscularis propria involvement on endoscopic ultrasound. Surgical specimen biopsy confirmed the diagnosis of multiple duodenal and jejunal GIST lesions and a metastatic NET in the duodenal lymph node. We report a rare case of a GIST detected in the duodenum during follow-up after the diagnosis and papillectomy of duodenal papilla NET. (Korean J Gastroenterol 2022;79:72-76)
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김현우 ( Hyun Woo Kim ),윤준식 ( Jun Sik Yoon ),유승정 ( Seung Jung Yu ),김태헌 ( Tae Heon Kim ),설재헌 ( Jae Heon Seol ),김단 ( Dan Kim ),정준영 ( Jun Young Jung ),정평화 ( Pyeong Hwa Jeong ),권훈 ( Hoon Kwon ),이홍섭 ( Hong Su 대한소화기학회 2020 대한소화기학회지 Vol.76 No.6
Duodenal varices are a serious complication of portal hypertension. Bleeding from duodenal varices is rare, but when bleeding does occur, it is massive and can be fatal. Unfortunately, the optimal therapeutic modality for duodenal variceal bleeding is unclear. This paper presents a patient with duodenal variceal bleeding that was managed successfully using percutaneous trans-splenic variceal obliteration (PTVO). A 56-year-old man with a history of alcoholic cirrhosis presented with a 6-day history of melena. Emergency esophagogastroduodenoscopy revealed a large, bluish mass with a nipple sign in the second portion of the duodenum. Coil embolization of the duodenal varix was performed via a trans-splenic approach (i.e., PTVO). The patient no longer complained of melena after treatment. The duodenal varix was no longer visible at the follow-up esophagogastroduodenoscopy performed three months after PTVO. The use of PTVO might be a viable option for the treatment of duodenal variceal bleeding. (Korean J Gastroenterol 2020;76:331-336)