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Case Reports : Benign Cephalic Histiocytosis: A Case Report
( Rafet Koca ),( Sibel Bektas ),( Cevdet Altinyazar ),( Tuna Sezer ) 대한피부과학회 2011 Annals of Dermatology Vol.23 No.4
Histiocytic skin disorders are usually classified as either Langerhans` cell histiocytosis (LCH) or non LCH, based on the pathology. Benign cephalic histiocytosis (BCH) is a rare type of non-Langerhans histiocytitic disorder and is characterized by self-healing multiple small eruptions of yellow to red-brown papules on the face and upper trunk. Histologic features of this disorder show dermal proliferation of histiocytes that have intracytoplasmic comma-shaped bodies, coated vesicles and desmosome-like structures. In this study, we report on a 7-month-old boy who contained small yellow-red papules on his face that spread to his upper trunk. The clinical and histologic features in this patient were consistent with BCH. (Ann Dermatol 23(4) 508~511, 2011)