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Kazuhiro Nakaso,Yoshiki Adachi,Emi Fusayasu,Koji Doi,Keiko Imamura,Kenichi Yasui,Kenji Nakashima 대한신경과학회 2012 Journal of Clinical Neurology Vol.8 No.3
Background Leber’s hereditary optic neuropathy (LHON) is a mitochondrial disorder with optic nerve atrophy. Although there are no other associated neurological abnormalities in most cases of LHON, cases of “LHON plus” have been reported. Case Report The proband was a 37-year-old man who had visual and gait disturbances that had first appeared at 10 years of age. He showed horizontal gaze palsy, gaze-evoked nystagmus, dysarthria,and cerebellar ataxia. Brain and orbit MRI disclosed atrophy of the optic nerve and cerebellum,and degenerative changes in the bilateral inferior olivary nucleus. Mutational analyses of mitochondrial DNA identified the coexistence of heteroplasmic G11778A and homoplasmic T3394C mutations. Conclusions These results suggest that the combination of G11778A and T3394C mutations leads to an atypical LHON phenotype.
miniTAO/ANIR Paα SURVEY OF LOCAL LIRGs
Tateuchi, Ken,Motohara, Kentaro,Konishi, Masahiro,Takahashi, Hidenori,Kato, Natsuko,Uchimoto, Yuka K.,Toshikawa, Koji,Ohsawa, Ryou,Kitagawa, Yutaro,Yoshii, Yuzuru,Doi, Mamoru,Kohno, Kotaro,Kawara, Kim The Korean Astronomical Society 2012 天文學論叢 Vol.27 No.4
ANIR (Atacama Near InfraRed camera) is a near infrared camera for the University of Tokyo Atacama 1m telescope, installed at the summit of Co. Chajnantor (5,640 m altitude) in northern Chile. The high altitude and extremely low water vapor (PWV = 0.5 mm) of the site enable us to perform observation of hydrogen $Pa{\alpha}$ emission line at $1.8751{\mu}m$. Since its first light observation in June 2009, we have been carrying out a $Pa{\alpha}$ narrow-band imaging survey of nearby luminous infrared galaxies (LIRGs), and have obtained $Pa{\alpha}$ for 38 nearby LIRGs listed in AKARI/FIS-PSC at the velocity of recession between 2,800 km/s and 8,100 km/s. LIRGs are affected by a large amount of dust extinction ($A_V$~ 3 mag), produced by their active star formation activities. Because $Pa{\alpha}$ is the strongest hydrogen recombination line in the infrared wavelength ranges, it is a good and direct tracer of dust-enshrouded star forming regions, and enables us to probe the star formation activities in LIRGs. We find that LIRGs have two star-forming modes. The origin of the two modes probably come from differences between merging stage and/or star-forming process.