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Relapsed Wilms’ tumor with multiple brain metastasis
Akın Akakın,Baran Yılmaz,Murat Şakir Ekşi,Özlem Yapıcıer,Türker Kılıç 대한소아청소년과학회 2016 Clinical and Experimental Pediatrics (CEP) Vol.59 No.no.sup1
Wilms’ tumor is the most common malignant renal tumor in childhood. The brain metastasis of a Wilms’ tumor with anaplastic histopathology is rare. We present the case of an 8-year-old girl with Wilms’ tumor, who presented with multiple brain metastases 5 years after her primary diagnosis. The brain masses were diagnosed after a generalized tonic-clonic seizure attack. The big solid mass in the cerebellum was resected, and whole-brain radiotherapy was performed, after which, she succumbed to her disease. In the case of clinical suspicion, cranial surveillance should be included in the routine clinical work-up for Wilms’ tumor. Combined aggressive therapy (surgery+radiotherapy+chemotherapy) should be applied whenever possible, for both better survival and palliative aspects.