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한국인 일차성 쇼그렌 증후군 환자의 선외 임상상의 분석
최병용 ( Byoong Yong Choi ),유종진 ( Jong Jin Yoo ),오혜진 ( Hye Jin Oh ),장유진 ( Yu Jin Jang ),이윤종 ( Yun Jong Lee ),송영욱 ( Yeong Wook Song ) 대한류마티스학회 2015 대한류마티스학회지 Vol.22 No.3
Objectives. To investigate the clinical findings upon initial diagnosis and extraglandular manifestations in Korean patients with primary Sjogren``s syndrome (pSS). Methods. We collected clinical and laboratory data from 238 pSS patients enrolled at Seoul National University Hospital, Seoul National University Bundang Hospital and Seoul Medical Center from March 2011 to December 2014. All patients met the American-European Consensus Group criteria for pSS. Results. Upon initial diagnosis, sicca symptoms (xerophthalmia or xerostomia) as the chief complaint were only observed in 129 (54.2%) pSS patients, while extraglandular manifestation was more common as the chief complaint in male patients or those with younger age (<40 years) than female or older patients (both p<0.05). Extraglandular manifestations were found in 178 (74.8%) patients, with musculoskeletal manifestations being most common (53.8%). Peripheral neuropathy in pSS patients was associated with Raynaud phenomenon and elevated serum total immunoglobulin G (IgG) levels (both p<0.05). Serum β2-microglobulin (β2-M) levels were significantly correlated with European League against Rheumatism (EULAR) Sjogren``s syndrome disease activity index, erythrocyte sedimentation rate and serum total IgG (all p<0.001), and were higher in patients with extraglandular manifestations than those without (p<0.05). Serum C3 levels were decreased in patients with extraglandular manifestation, compared to those without (p<0.05). Malignant lymphoma was found in Korean pSS patients (1.7%) and associated with elevated serum β2-M levels (p<0.0001). Conclusion. Extraglandular manifestations were common in pSS patients and may be a diagnostic tool for male or younger pSS patients. Serum β2-M levels can be useful markers for monitoring pSS patients. (J Rheum Dis 2015;22:167-174)
만성 염증성 탈수초성 다발신경병증과 헤노흐-쇤라인 자반증을 동반한 강직성 척추염
최병용 ( Byoong Yong Choi ),권현미 ( Hyun Mi Kwon ),성정준 ( Jung Jun Sung ),박성혜 ( Seong He Park ),송영욱 ( Yeong Wook Song ) 대한내과학회 2012 대한내과학회지 Vol.83 No.4
Peripheral nervous system dysfunction is a rare complication in Henoch-Schonlein purpura, but it tends to recover spontaneously without treatment. A 78-year-old man who had ankylosing spondylitis presented with Henoch-Schonlein purpura associated with progressive sensorimotor polyneuropathy. He was diagnosed with chronic inflammatory demyelinating polyneuropathy, which did not improve despite intravenous immunoglobulin therapy. We describe a case of Henoch-Schonlein purpura, accompanied by chronic inflammatory demyelinating polyneuropathy in a patient with ankylosing spondylitis. (Korean J Med 2012;83:538-542)
정희원 ( Hee Won Chung ),유종진 ( Jong Jin Yoo ),최병용 ( Byoong Yong Choi ),조현정 ( Hyun Jung Cho ),강은하 ( Eun Ha Kang ),송영욱 ( Yeong Wook Song ),이윤종 ( Yun Jong Lee ) 대한류마티스학회 2013 대한류마티스학회지 Vol.20 No.5
Primary Sjogren`s syndrome (pSS) is characterized by chronic inflammation and dysfunction in exocrine organs; however, it also has protean clinical features, including neuropsychiatric symptoms. A major neurological manifestation is peripheral neuropathy and involvement of the central nervous system is uncommonly described in pSS. A 52-year-old female was admitted because of depression, dysarthria, gait abnormality, and memory disturbance, which had developed over two months, and was diagnosed as pSS. She was treated successfully with high-dose glucocorticoid and cyclophosphamide pulse therapy without recurrence during the follow-up period of two years. Herein, we describe the first Korean case of pSS presenting with rapidly progressive cognitive impairment along with a review of the literature.
탄광부 진폐증 환자에서 맞춤형 호흡 재활 치료 프로그램의 임상적 효용성
정희 ( Hee Cheong ),이정민 ( Jeong Min Lee ),박인기 ( In Ki park ),김종규 ( Jong Kyu Kim ),전근재 ( Geun Jae Jeon ),김주령 ( Ju Ryung Kim ),김지홍 ( Ji Hong Kim ),최병용 ( Byoong Yong Choi ) 대한내과학회 2014 대한내과학회지 Vol.87 No.6
Background/Aims: It is unknown whether pulmonary rehabilitation (PR) is an effective intervention to manage coal worker pneumoconiosis (CWP). We evaluated the efficacy and safety of an individualized PR program in 53 patients with CWP hospitalized in two medical institutions. Methods: The PR program consisted of upper and lower extremity exercises to improve exercise endurance and skeletal musculoskeletal strength. All subjects performed treadmill and ergometer exercise with steady loading weights three times/week for 12 weeks. The following tests were performed before and after the study to investigate the efficacy of the PR program: modified Borg scale, pulmonary function test, mid-thigh circumference, maximum muscular strength, 6-min walk distance (6MWD), and the St. George’s Respiratory Questionnaire (SGRQ), Korean version. Results: Forty patients (75.5%) completed their PR programs. They improved significantly on the modified Borg scale, mid thigh circumference, maximum muscular strength, 6MWD (all p < 0.000), and SGRQ (p = 0.007), however, no significant improvement was observed on the pulmonary function test. A significant improvement in dyspnea (p = 0.004) and 6MWD (p = 0.002) was observed in 12 patients with forced expiratory volume in 1 sec < 60%. The PR program with smoking cessation resulted in significantly more improvement on the 6MWD (p < 0.0001) and the SGRQ score (p = 0.002), as compared to those of patients who did not quit smoking. Conclusions: Our results show that an individualized 12-week PR program improves exercise capacity and quality of life for patients with CWP. (Korean J Med 2014,87:690-697)
성인형 스틸병과 유사한 임상양상을 보인 다발성 골 결핵 1예
조진경 ( Jin Kyeong Cho ),김민성 ( Min Sung Kim ),신진호 ( Jin Ho Shin ),정연상 ( Yeon Sang Jeong ),김준완 ( Joon Wan Kim ),최재필 ( Jae Phil Choi ),최병용 ( Byoong Yong Choi ) 대한내과학회 2014 대한내과학회지 Vol.86 No.6
A 46-year-old man was admitted to our hospital because of a fever of unknown origin. The patient had a skin rash, arthralgia, and hepatosplenomegaly. Laboratory tests showed leukemoid leukocytosis, a high serum ferritin level (31,200 ng/mL), and abnormal liver function tests. He was initially diagnosed with adult-onset Still`s disease (AOSD). However, imaging studies incidentally detected a cold abscess involving the 11th thoracic vertebra. A biopsy of the abscess revealed histologically granulomatous caseous necrosis, positive for M. tuberculosis by polymerase chain reaction. We present a patient with musculoskeletal tuberculosis (TB) that clinically mimicked AOSD. In TB-endemic countries, extrapulmonary TB should be included in the differential diagnosis of AOSD. (Korean J Med 2014;86:785-790)