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자가 면역성 저혈당으로 발현한 전신성 홍반성 루푸스와 간질성 폐질환을 동반한 B형 인슐린 저항 증후군
장지원 ( Ji Won Jang ),백초옥 ( Cho Ok Baek ),김선민 ( Seon Min Kim ),이창훈 ( Chang Hun Lee ),국민하 ( Min Ha Kook ),양희찬 ( Hee Chan Yang ),김인재 ( In Jae Kim ),임성균 ( Sung Kyun Yim ),조인진 ( In Jin Cho ),진흥용 ( Heung Yon 전북대학교 의과학연구소 2011 全北醫大論文集 Vol.35 No.2
Autoimmune forms of hypoglycemia which characterized by the presence of autoantibodies to insulin or insulin receptor are uncommon condition. Systemic lupus erythematosus (SLE) is a connective tissue disorder of unknown etiology accompanied by the presence of several kinds of autoantibodies and results in immune-mediated organ damage of multiple sites. We describe herein an unusual case of SLE with pulmonary manifestation presenting as hypoglycemia due to anti-insulin receptor antibodies. A 38-year-old Korean woman suffered an episode of unconsciousness and was admitted to hospital where blood glucose was found to be 18mg/dL. During hypoglycemic episode, her serum insulin level was inappropriately high (2,207.1 pmol/L; normal range: 18.173 pmol/L) and C-peptide level was elevated (1.7 nmol/L; normal range: 0.37.1.47 nmol/L). Further blood test revealed the presence of antinuclear antibody, anti-double stranded DNA antibody, anti-Ro/SSA, anti-La/SSB, anti-ribonecleoprotein, anti-insulin receptor antibody. Computed tomography scan for abdomen which was attempted at tumor localization such as insulinoma revealed ground-glass opacities in both lower lungs, while there was no abnormal finding in the abdomen. For a definitive diagnosis of the lung lesion, video associated thoracoscopic surgery was performed and the histopathological findings showed a pattern of fibrotic nonspecific interstitial pneumonia.