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유향석 ( Hyang Suk You ),조현호 ( Hyun Ho Cho ),김원정 ( Won Jeong Kim ),문제호 ( Je Ho Mun ),송마가렛 ( Margaret Song ),김훈수 ( Hoon Soo Kim ),고현창 ( Hyun Chang Ko ),김병수 ( Byung Soo Kim ),김문범 ( Moon Bum Kim ) 대한피부과학회 2014 大韓皮膚科學會誌 Vol.52 No.6
Department of Dermatology, School of Medicine, Pusan National University1, Medical Research Institute, Pusan National University Hospital2, Busan, Korea Background: A variety of benign and malignant tumors can occur in the nail apparatus, causing nail deformities and growth disorders. Clinical diagnosis of nail apparatus tumors can be difficult because of their similar clinical appearance. Objective: The aim of this study was to determine the types and frequency of nail apparatus tumors and to assess the types and frequency of nail alterations induced by tumors. Methods: We retrospectively reviewed the medical records, clinical photos, and histologic slides of 165 patients with nail apparatus tumors who had visited Pusan National University Hospital between January 2002 and August 2012. Results: The most frequently diagnosed benign tumors were digital mucous cysts (22.4%), glomus tumors (21.8%), and subungual exostoses (8.5%). The most common malignant tumors were melanomas (17.0%), squamous cell carcinomas (4.9%), and Bowen`s disease (3.0%). We observed nail plate alterations in 80.6% of the cases. All cases of melanomas, fibrous tumors, and subungual exostoses produced nail alterations. Most tumors were treated with surgical management. Conclusion: Although the sample size of this study was small, this is the first Korean dermatologic trial to identify nail apparatus tumors. The study findings may prove useful in the clinical diagnosis of various nail apparatus tumors. (Korean J Dermatol 2014;52(6):381∼386)
동일 부위에 발생한 유방외 파젯병과 뾰족콘딜로마의 연관성
유향석 ( Hyang-suk You ),하대룡 ( Dae-lyong Ha ),김정민 ( Jung-min Kim ),김건욱 ( Gun-wook Kim ),문제호 ( Je-ho Mun ),송마가렛 ( Margaret Song ),고현창 ( Hyun-chang Ko ),김병수 ( Byung-soo Kim ),김문범 ( Moon-bum Kim ),김훈수 ( Hoo 대한피부과학회 2018 大韓皮膚科學會誌 Vol.56 No.1
Extramammary Paget’s disease (EMPD) is a rare skin neoplasm, which usually affects the anogenital region of older individuals. Condyloma accuminatum is a very common benign human papilloma virus (HPV)-associated keratinous neoplasm affecting the anogenital region of children and adults. To our knowledge, two cases of simultaneous occurrence of EMPD and condyloma accuminatum have been reported in the written English literature until now. We report a case of a 58-year-old man with simultaneous occurrence of EMPD and condyloma accuminatum in a lesion for the first time in Korea. Histologic, immunohistochemical and HPV-PCR test results were also described to analyze the development of the lesion and the correlation between EMPD and condyloma accuminatum. (Korean J Dermatol 2018;56(1):53∼56)
유향석 ( Hyang Suk You ),좌승욱 ( Seung Wook Jwa ),김훈수 ( Hoon Soo Kim ),고현창 ( Hyun Chang Ko ),김병수 ( Byung Soo Kim ),김문범 ( Moon Bum Kim ),송마가렛 ( Margaret Song ) 대한피부과학회 2012 대한피부과학회지 Vol.50 No.12
Linear lesions of discoid lupus erythemaosus (DLE), subacute cutaneous lupus erythematosus or tumid lupus erythematosus, following the lines of Blaschko, are called linear cutaneous lupus erythematosus (LCLE). Lesions of LCLE appear as linear unilateral erythematous plaques predominantly on the face. Neck, trunk or the extremities may also be affected. Histological findings show hyperkeratosis with follicular plugging, epidermal atrophy, hydropic degeneration and dense perivascular infiltration of the inflammatory cells, including lymphocytes and histiocytes. To our knowledge, four cases of linear lupus erythematosus have been reported in Korean literature. We report three patients diagnosed with LCLE. (Korean J Dermatol 2012;50(12):1064∼1068)
유향석 ( Hyang Suk You ),문제호 ( Je Ho Mun ),좌승욱 ( Seung Wook Jwa ),송마가렛 ( Mar Ga Ret Song ),김훈수 ( Hoon Soo Kim ),고현창 ( Hyun Chang Ko ),김문범 ( Moon Bum Kim ),김병수 ( Byung Soo Kim ) 대한피부과학회 2013 대한피부과학회지 Vol.51 No.7
Various modalities have been used for the treatment of psoriasis, including phototherapy. The choice of psoriasis treatment is based on the characteristics of the lesions, locations and amount of involved body surface area. Narrowband ultraviolet (UV) B therapy is a widely used and highly efficient method for psoriasis. But, large areas of unaffected skin may be irradiated along with the psoriatic lesions during phototherapy. The 308-nm excimer laser is a further development of narrowband UVB and was reported to be an effective and safe treatment for localized psoriasis. We experienced an excellent effect without significant adverse reactions of 308-nm excimer laser in a 9-year-old patient with palmoplantar psoriasis who was recalcitrant to oral cyclosporine and topical calcipotriol/ betamethasone treatment. (Korean J Dermatol 2013;51(7):527∼530)
하대룡 ( Dae-lyong Ha ),진현주 ( Hyunju Jin ),유향석 ( Hyang-suk You ),심우행 ( Woo-haing Shim ),김정민 ( Jeong-min Kim ),김건욱 ( Gun-wook Kim ),김훈수 ( Hoon-soo Kim ),고현창 ( Hyun-chang Ko ),김병수 ( Byung-soo Kim ),김문범 ( M 대한피부과학회 2018 大韓皮膚科學會誌 Vol.56 No.4
Unilateral linear capillaritis (ULC) is a rare variant of pigmented purpuric dermatosis (PPD). ULC is clinically characterized by unilateral linear macules on the lower extremities, which fade spontaneously. We present three patients with linearly distributed purpuric macules on only one side of the lower extremities. Skin biopsy showed histopathological features of PPDs. We diagnosed ULC based on these clinicopathological findings. For all patients, the skin lesions began to fade spontaneously within several months to a few years after onset. ULC has been reported rarely, with only about 20 cases worldwide and no cases described in the Korean literature. (Korean J Dermatol 2018;56(4):273∼275)
TRPS1 유전자의 새로운 과오돌연변이를 보인 제 3형 모발-비-수지 이형성 증후군
노동영 ( Dongyoung Roh ),김태욱 ( Tae-wook Kim ),박성민 ( Sung-min Park ),이현주 ( Hyun-joo Lee ),진현주 ( Hyunju Jin ),유향석 ( Hyang-suk You ),심우행 ( Woo-haing Shim ),김건욱 ( Gun-wook Kim ),김훈수 ( Hoon-soo Kim ),김병수 ( By 대한피부과학회 2018 大韓皮膚科學會誌 Vol.56 No.8
Trichorhinophalangeal syndrome (TRPS) is a rare autosomal dominant hereditary disease caused by mutations in the TRPS1 or the EXT1 gene. Patients show 3 different forms (TRPS I-TRPS III) of this condition sharing similar clinical features including sparse hair, a bulbous nose, an elongated philtrum, short stature, and shortened phalanges. A 10-year-old girl presented with sparse hair and thin hair shafts since birth. She also showed a bulbous nose, an elongated philtrum, brachydactyly of the great toes, and a short stature. Radiological examination showed cone-shaped epiphyses and shortened phalanges. Genetic analysis revealed a novel missense mutation c.2759G>C (p.Trp920Ser) in the TRPS1 gene. We diagnosed this patient with TRPS type III. To our knowledge, only 3 reports have described a genetically analyzed TRPS1 gene mutation among the 11 reported cases of TRPS in the Korean literature. Furthermore, we identified a novel missense mutation in the TRPS1 gene. (Korean J Dermatol 2018;56(8):494∼498)