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변승주 ( Seung Joo Byun ),강현우 ( Hyoun Woo Kang ),차주경 ( Joo Kyoung Cha ),류수령 ( Soo Ryeong Ryoo ),이정현 ( Jeong Hyeon Lee ),김도연 ( Do Yeon Kim ),김어진 ( Eo Jin Kim ) 대한소화기학회 2016 대한소화기학회지 Vol.67 No.5
Mucosa-associated lymphoid tissue (MALT) lymphoma is found in various organs as extranodal B cell lymphoma. The gastrointestinal tract is the most commonly involved extranodal site in MALT lymphoma. However, primary esophageal MALT lymphoma is very rare. In addition, few cases with metachronous gastric involvement have been reported. A 55-year-old man was diagnosed with MALT lymphoma by surveillance esophagogastroduodenoscopy. A 5 cm esophageal submucosal tumor-like lesion was incidentally revealed by screening esophagogastroduodenoscopy two years prior. Esophagogastroduodenoscopy showed a cylindrically elongated submucosal mass with normal overlying mucosa in the mid esophagus. He underwent surgery to confirm the diagnosis. The pathologic diagnosis was esophageal MALT lymphoma. He was treated with radiation, which achieved complete remission. Esophagogastroduodenoscopy and chest computed tomography were performed every three to six months, with no evidence of recurrence for 18 months. After 21 months, several elevated gastric erosions were found on the great curvature and posterior sides of the midbody and confirmed as MALT lymphoma pathologically. Here we report a case with MALT lymphoma metachronously involving the esophagus and stomach. (Korean J Gastroenterol 2016;67:257-261)
홍경희 ( Kyong Hee Hong ),이준규(교신저자) ( Jun Kyu Lee ),변승주 ( Seung Joo Byun ),정재우 ( Jae Woo Jung ),한인웅 ( In Woong Han ),정진희 ( Jin Hee Jung ),김어진 ( Eo Jin Kim ) 대한소화기학회 2015 대한소화기학회지 Vol.66 No.2
Leukemoid reaction is defined as leukocytosis exceeding 50,000 cells/mm3. When it occurs in a patient with a malignancy, secondary causes such as infections, drugs, hematologic diseases and hemorrhage need to be ruled out. After excluding such causes, paraneoplastic leukemoid reaction can be considered as a diagnosis of exclusion. Paraneoplastic leukemoid reactions have been described in association with lung, gastrointestinal, genitourinary and head and neck cancers. However, pancreatic cancer with leukemoid reaction has been rarely reported. We diagnosed a case of a 55-year-old Korean woman with extreme leukocytosis associated with advanced pancreatic cancer. (Korean J Gastroenterol 2015;66:116-121)
십이지장 위장관기질종양 내에서 발견된 혈관내큰B세포림프종 1예
이정현 ( Jeong Hyeon Lee ),이준규 ( Jun Kyu Lee ),류수령 ( Soo Ryeong Ryoo ),변승주 ( Seung Joo Byun ),한강민 ( Kang Min Han ),정진희 ( Jin Hee Jung ),한인웅 ( In Woong Han ),권재현 ( Jae Hyun Kwon ),김어진 ( Eo Jin Kim ) 대한췌담도학회 2016 대한췌담도학회지 Vol.21 No.4
혈관내큰B세포림프종은 악성 림프구의 혈관 내 성장을 보이는 드문 질환으로, 말초혈액 또는 혈관 외 종괴를 보이지 않는다. 이 림프종은 빠른 파종 및 공격적 성향 때문에 나쁜예후를 가진다. 그러나 질병특유소견이 없어 진단이 어려운 실정이다. 저자들은 십이지장 위장관기질종양의 수술 검체내에서 혈관내큰B세포림프종이 진단된 증례를 발견하였기에 문헌고찰과 함께 보고하는 바이다. Intravascular large B-cell lymphoma (IVLBCL) is a rare disease of intravascular growth of malignant lymphocytes without an obvious extravascular tumor mass or existence in peripheral blood. It has poor prognosis due to its aggressive behavior and rapid systemic dissemination. But there is no pathognomonic finding, diagnosis of IVLBCL is still challenging. Here we report a case of IVLBCL found within a resected specimen of duodenal gastrointestinal stromal tumor.