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6 종류의 생식세포와 육종성 변화를 보인 혼합 생식세포종 1 예
방금화(Chin Hua Fang),박성민(Sung Min Park),송경은(Kyung Eun Song),송은섭(Eun Seop Song),임영구(Young Koo Lim),황성욱(Seong Ook Hwang),고승권(Seung Kwon Koh),조숙(Sook Cho),이우영(Woo Young Lee) 대한산부인과학회 1999 Obstetrics & Gynecology Science Vol.42 No.1
Malignant germ cell tumors of the ovary are uncommon neoplasms. Although 20-25% of all ovarian tumors are derived from germ cells, only about 3% of germ cell tumors are malignant. Mixed germ cell tumors contain at least two malignant germ cell elements. These lesions should be managed with combination chemotherapy, preferably BEP. Recently we experienced a case of mixed germ cell tumor with 6 components of germ cell and sarcomatous change in a 11 year old girl. Preoperative CA-125, B-hCG, aFP, LDH, a-1-antitrypsin were elevated and the final pathologic report was mixed germ cell tumor composed of endodermal sinus tumor, embryonal carcinoma, mature and immature teratoma, choriocarcinoma, dysgerminoma and sarcomatous change, Postoperative chemotherapy with 6 courses of BEP regimen was performed and all tumor markers became normal after 4 courses of chemotherapy. What we interested in this case was several components of germ cells and sarcomatous change and the sarcomatous change might be derived from the mature cystic teratoma component, so we present this case with a brief review of the literatures here.