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조재훈(Je Hun Jo),박영복(Young Bock Park),박태형(Tae Hyoung Park),장원연(Won Yeon Jang),김도균(Do Gyun Kim),김경원(Kyoung Won Kim),이동기(Dong Ki Lee),윤혜원(Hae Won Yoon),김동훈(Dong Hun Kim),김미운(Mi Woon Kim),박성태(Sung Tae Park 대한산부인과학회 2001 Obstetrics & Gynecology Science Vol.44 No.5
The Complete testicular feminization syndrome is a hereditary syndrome characterized clinically by female phenotype with 46, XY karyotype and bilateral testes. There is a congenital insensitivity to androgens, transmitted by means of a maternal X-linked recessive gene responsible for the androgen intracellular receptor. Therefore, androgen induction of Wolffian duct development does not occur. However, anti-mullerian hormone activity is present and the individual does not have mullerian development. Principle of treatment is reinforced to live normal female life. This is a case report of testicular feminization syndrome with rudimentary salpinx with the brief review of literatures.