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정성원 ( Jeong Seong Won ),이유민 ( Lee Yu Min ),박무림 ( Park Mu Lim ),이명수 ( Lee Myeong Su ),백승훈 ( Baeg Seung Hun ),안선호 ( An Seon Ho ),송주흥 ( Song Ju Heung ) 대한내과학회 2004 대한내과학회지 Vol.66 No.3
Paroxysmal nocturnal hemoglobinuria (PNH) is a acquired clonal disorder of the hematopoietic stem cells characterized by chronic intravascular hemolysis, venous thrombosis, deficient hematopoiesis. Kidney involvement is usually benign and secondary to chronic deposition of hemosiderin. But, acute renal failure may rarely occur in association with a hemolytic crisis or thrombotic complication. Hemolytic crisis is precipitated by nonspecific factors, such as infection, surgery and transfusion. A 69-year-old man was admitted to our hospital who developed acute renal failure after operation of anal fistula. He was diagnosed with PNH accompanied with deep vein thrombosis later. After being treated by hemodialysis and oral low dose steroid, he was discharged with full recovery of renal function. But, he frequently was developed acute renal failure with crisis of PNH despite taking low dose steroid. So, we report a case of PNH with recurrent acute renal failure without precipitating factors.
이용국 ( Lee Yong Gug ),이용엽 ( Lee Yong Yeob ),손준광 ( Son Jun Gwang ),선홍주 ( Seon Hong Ju ),한상우 ( Han Sang U ),이지신 ( Lee Ji Sin ),박무림 ( Park Mu Lim ) 대한내과학회 2003 대한내과학회지 증례 특집호 65-5 부록3 Vol.0 No.-
Pernicious anemia is caused by the absence of intrinsic factor from autoimmune destruction of parietal cells. Patients with pernicious anemia are predisposed to the development of gastric cancer. We report here a case of pernicious anemia with early gastr