Hypophosphatasia 환아의 치료 증례

최병제,최형준,이제호,김기덕,박수정 大韓小兒齒科學會 1998 大韓小兒齒科學會誌 Vol.25 No.3

1. Hypophosphatasia 는 골조직 및 치아조직의 비정상적인 석회화를 나타내는 대사장애로, 특징적구강내 소견 인 우치의 조기탈락 양상으로 치과에서 조기진단이 가능하다. 2. 본 증례에서 상악궁 확장을 동반한 의치 제작으로 심미적, 기능적으로 양호한 결과를 얻었으며, 영구치열기 까지 장기적 관찰 및 치료가 필요할 것으로 사료된다. hypophosphatasia is a rare metabolic disorder which manifests characteristics such as abnormal mineralization of bone and dental tissues, diminished serum and tissue alkline phosphatase, and increased urinary secretion of PEA. It ingerited as an autosomal recessive or dominant trait and occurs in all races. In general, hypophosphatasia can be classified in 4 subtypes which are the perinatal, infantile, childhood, adult type depending upon the age at presentation and severity. In young children with Hypophosphatasia the long bones show irregular defects, and the skull showes poor calcification. In older children with premature closure of the skull sutures there may ve multiple lucent area called gyral or convolutional markings, described as resimbling beaten copper, presumably resulting from increased intracranial pressure,Examination of the jaws reveals a generalized lucency of the maxilla and mandible, the cortical bone and lamina dura are thin, and the alveolar bone may be deficient. Clinical features of Hypophosphatasia imclude premature loss of deciduous teeth, especially incisors, hypoplasia of aplasia of root cementum, enamel hypoplasia, irregular calcification of dentin, large pulp chamber, and resorption of marginal alveolar bone and roots. Our report involves a patient with a chief complaint of early loss of both Mx. and Mn. deciduous ncisors. after conducting a through clinical and radiographic examination this patient was referred to pediatrics under the suspicion of hypophosphatasia, the diagnosis proved to be correct and successful results were accomplished through a denture made to improve esthetics and function.

Seeds의 Crystallinity가 Cordierite의 상변태에 미치는 영향

최태현,전병세,이성우 慶南大學校 附設 工業技術硏究所 1994 硏究論文集 Vol.12 No.-

고밀도이며 고순도인 cordierite를 제조하기 위하여 solution sol-gel법과 α-cordierite의 seeding을 이용하였다. 시료를 분말과 monolith로 나누어 실험을 행하여 seed의 품질이 cordierite의 μ-type에서 α-type로의 상변태와 밀도에 관해서 각각 어떠한 영향을 미치는가에 대해서 알아보았다. 연구결과, 1000℃에서 합성한 seed용 분말보다 1300℃에서 합성한 seed용 분말이 더 α-cordierite 결정에 접근되어 있었고, 1300℃에서 합성한 seed를 첨가한 분말이 여러 범위의 온도에서 α-cordierite결정으로 가장 잘 발달하였으며, monolith의 경우 역시 1300℃에서 합성한 seed를 첨가한 것이 높은 밀도를 가지는 것으로 나타났다. 그러므로 cordierite의 homogeneity와 밀도는 첨가하는 seed의 crystallinity에 크게 좌우된다고 하겠다. Solution sol-gel(SSG) method and seeding were used to fabricate homogenious α-cordierite with high purity. The cordierite powders prepared by SSG and heat-treating at various temperature ranging 1000-1300℃ were added in the mixed or reacted with solution for seeding. Seed powder synthesized at 1300℃ was well developed to α-cordierite rather than any other seed powders at below 1300℃ and the quantity of α-phase was highest in the powder heat-treated at 1300℃ which had been added by seeding at 1300℃. The densities of all the monoliths were high because of existense of other phases like spinel. Therefore, the homogenity of resultant oxides depends on the crystallinity of seed.

중학교 사회과 경제 관련 교육과정 내용 요소 분석

최병모,박형준,전희옥 한국경제교육학회 2004 경제교육연구 Vol.11 No.2

경상돌기연장증 2례

최종욱,권기환,전병선,김정준,최건 한국의학사 1998 診斷과治療 Vol.18 No.9

Lesch-Nyhan syndrome 환아의 oral self-mutilation 에 대한 증례보고

최병재,최형준,이제호,전진용 大韓小兒齒科學會 1999 大韓小兒齒科學會誌 Vol.26 No.1

1. 하순에 심한 self-mutilation wound를 야기한 Lesch-Nyhan Syndrome 환아에서 상하악 유전치에 치관부 절단 및 치수 절세술을 시행하여 치아에 의한 자해를 방지하였다. 2. 장치를 이용한 치료가 어려운 경우 발치가 고려되기도 하나 본 증례에서는 발치보다 보존적인 술식으로 만족할 만한 결과를 얻었다. Self-injurous behavior is defined as deliberate harm to one's own body without suicidal intent. It usually occurs as head banging or hitting, skin cutting, or finger biting and includes ocular, genital and oral self-mutilation. Lesch-Nyhan syndrome is a rate X-linked recessively inherited disorder, caused by complete absence of hypoxanthin-guanine phosphoribosyl transferase(HPRT) activity. Clinical presentation is characterized by mental retardation, chorea, athetosis, hyperuricemia, uricosuria and self-mutilating behavior. In these patients, the most typical feature is loss of tissue from biting themselves, even though they are not insensitive to pain. The dental management of self-mutilation includes treatment with appliances such as soft mouthgrard or lip bumper, extraction of all the teeth, and orthognathic surgery. We report a 25-month-old boy who was a known case of Lesch-Nyhan syndrome and presented with severe self-mutilation wound on his lower lip. Vital pulpectomy and coronal resection was done as a more conservative approach than extracting all primary anterior teeth. Due to maintaining the root portion of the teeth in the bone, it is expected that the normal growth of the alveolar bone will be achieved.

악교정 수술시 컴퓨터를 이용한 측면두부규격방사선사진 분석 및 예측의 유용성에 관한 연구

최병준,김여갑 大韓顎顔面成形再建外科學會 2003 Maxillofacial Plastic Reconstructive Surgery Vol.25 No.4

Analysis and prediction on lateral cephalometric must be necessary to know present states and it is important to decide method and magnitude of real orthognathic surgery. The purpose of this study is to evaluate accuracy that post-surgical lateral cephalometric analysis compared with simulated surgical lateral cephalometric analysis using orthognathic surgery prediction system (V-ceph™version 3.0). The result as follow Skeketal position change showed significantly difference between predicted and actual means.(12 of 19). Dental position change showed significantly difference between predicted and actual means.(5 of 9).The angles which were measured among three points showed significantly difference between predicted and actual means.(13 of 18). The distances which were measured between two points significantly difference between predicted and actual means.(4 of 8). None of 2 measurement for ratio showed significantly difference between predicted and actual means. Overall 17 of 28 measurements showed significant difference in means As the result of this study, it was inappropriate to apply prediction system in clincal situation. But the difference was not servere, prediction system could show out line of post-surgical reult approximately. So, it is possible to predict the post-surgical result simply, and to explain the surgery to patient.

F. 뒤렌마트의 연극론(Dramaturgie) 연구

최병준 西原大學校 1989 西原大學 論文集 Vol.23 No.-

Friedrich Durrenmatt ist mehr Theater-Praktiker als Theoretiker. Seine theaterische Auβerungen sind daher in der Erfahrung mit dem Theater begrundet oder nur Reaktionen auf gegen ihn gerichtete Vowurfe. Er lehnt das Aristotelische Theater ab. Er behauptet, die Aristotelische Tragodie sei nicht mehr die zeitangessene Theaterform, die heutige Welt, die ungestalter, ungeheuer, anonym geworden sei, auf der Buhne darzustellen. Nur die Komodie habe noch mehere Moglichkeiten. In seiner Komodien wird das in der Wirklichkeit vorgefundene Material in den Bereich des Komischen, d.h. des Grotesken und Paradoxen transponiert,das durch die Nichtidentifikaton de Zuschauer den Abstand herstellt. Brecht und Durrenmatt erkennen gemeinsam die Notwendichkeit der Verfremdungsefekt an. Aber die verfremdenden Methoden des Epischen Theaters bei Bercht werden in den Komodien Durrematts durch Komik und Groteske ersetzt. Der wesentliche Unterschied zwischen beiden Autoren liegt in der kontraren Weltsicht begrundet. Brechts Ausgangspunkt ist eine durch die menschliche Vernunft veranderbare Welt. Er versucht durch sein Theater das Pubikum aufzuklaren und die Gesellschaft zu verandern. Bei Durrenmatt dagegen ist die heutige Welt fur den einzehlen undurchschaubar geworden. Er sieht im Theater nur eine Moglichkeit, die Welt durchschaubar zu machen. Daher kann er dem Publikum nur Modelle liefern, die es auf seine eigenen Fall beziehen und deuten kann.

학교 경제교육 방향 탐색을 위한 델파이 조사 연구

최병모,김정호,이준혁 한국경제교육학회 2005 경제교육연구 Vol.12 No.1

복합 치아종에 관한 증례보고

최형준,최병재,손흥규,양호정 大韓小兒齒科學會 1995 大韓小兒齒科學會誌 Vol.22 No.2

The odontoma is relatively a common odontogenic tumor. It has come to mean as a growth in which both the epithelial and the mesenchymal cell exhibit complete differentiation, with the result that functional ameloblast and odontoblast form enamel and dentin. The etiology of it is unknown, but it has been suggested that local trauma or infection may lead to the production of such a lesion. Odontma is divided into 2 types. One is compound odontoma that is at least superficial anatomic simiarity to normal teeth, and the other is complex odontoma, that calcified dental tissues are simply an irregular mass bearing no morphologic similarity even to rudimentary teeth. Somtimes this malformation is not easily identified because its lacking of calcification. So, if permanant tooth is delayed to erupt, one should take a careful look the radiographic film to find that whether the cause of it is odontoma or not. In this case report, 3 patients with odontoma who visited Dept. of Pediatric Dentistry in Yonsei Dental College, were treated by means of surgical removal. The obtained results were as follows: 1. The odontoma is usually related to impacted tooth, and it is occurred neighboring to the crown of impacted tooth that have normally developed. So, in the case of missing tooth and delayed eruption, its presence should be investigated. 2. The odontoma can be seen vaguely radiographically, so, it is difficulty to make diagnosis. 3. The treatment of odontoma is a surgical removal. And, if it is completely removed, its occurrence is rare. 4. In the case of impacted tooth being associated with compound odontoma, continuous management is necessary for the eruption of impacted tooth after the surgical extraction of odontoma. 5. It resembles the ameloblastic odontoma radigraphically, and if it is the case, the treatment may vary, so the confirmation through histologic examination after removal of mass is necessary.

Friedrich Durrenmatt의 演劇技法 : "老부인의 訪問"을 중심으로

최병준 西原大學校 1985 西原大學 論文集 Vol.15 No.-

Der Ausgangspunkt der Durrenmattischen Dramaturgie ist die Frage:Wie laβt sich unsere heutige Welt noch auf der Theaterbuhne darstellen? Durrenmatt behauptet, die klassische Form der Tragodie von Aristotelischer Tradition ist keine zeitangemessene Theaterform, um die heutige Welt auf der Buhne darzustellen. eines der wichtigsten Grunde dafur ist, daβ heute die tragische Helden fehlt, die die Welt reprasentieren konnen. Als eine mogliche Theater form bleibt bei uns nur die Komodie, die Durrenmatt "Welttheater" bzw. "Zeitstuck" nennt. Durrenmatt verwendet fur seine Komodie einerseits bekannte Stoffe, die er aus der Geschichte oder aus literarisch bereit geformten Vorlagen bezieht, Andererseits erfindet er seine Stoffe frei, einem Einfall folgend. Bei der Konzeption der Stoffe von seiner Komodien ist fur durrenmatt "Einfall" die Zentralbegriff. Unter dem "Einfall" versteht durrenmatt eine erfundence, nicht ge fundene, Handlung, die sich nicht in der Vergangenheit abspielt und nicht auf Mythen oder andere uberlieferungen zuruckgeht. Fur Durrenmatt ist der Ort der Handlung von groβer Bedeutung. Bei der Auswahl eines bestimmten Schauplatzes werden reale, historisch festgelegte Orte vernachlassigt, also "entstofflicht". Aber bei Durrenmatt bedeutet die Buhne in besonderer Weise die Welt. Diese Welt, die Durrenmatt als Ort der Handlung auswahlt, ist insgesamt verfallen, schmutzig, abstoβend. durrenmatts Komodien haufig durch das "Groteske" oder das "Paradoxe" charakterisiert. das Groteske und das Paradoxe in der Entwicklung der Handlung sind bei durrenmatt nicht nur Darstellungsmittel, das den "DistanzEffekt" erwirkt, sondern auch eine Ausdruk seiner Weltauffassung.