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증례 : 류마티스 ; 만성 염증성 탈수초성 다발신경병증과 헤노흐-쇤라인 자반증을 동반한 강직성 척추염 1예
최병용 ( Byoong Yong Choi ),권현미 ( Hyun Mi Kwon ),성정준 ( Jung Jun Sung ),박성혜 ( Seong He Park ),송영욱 ( Yeong Wook Song ) 대한내과학회 2012 대한내과학회지 Vol.83 No.4
Peripheral nervous system dysfunction is a rare complication in Henoch-Schonlein purpura, but it tends to recover spontaneously without treatment. A 78-year-old man who had ankylosing spondylitis presented with Henoch-Schonlein purpura associated with progressive sensorimotor polyneuropathy. He was diagnosed with chronic inflammatory demyelinating polyneuropathy, which did not improve despite intravenous immunoglobulin therapy. We describe a case of Henoch-Schonlein purpura, accompanied by chronic inflammatory demyelinating polyneuropathy in a patient with ankylosing spondylitis. (Korean J Med 2012;83:538-542)