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Massive Empyema Associated With Transient Hypogammaglobulinemia of Infancy and IgA Deficiency
박건,이경일,이미희,이준성,김지창 대한의학회 2009 Journal of Korean medical science Vol.24 No.2
Transient hypogammaglobulinemia of infancy (THI) is originally defined as a physiological maturation defect of immunoglobulin G (IgG) production that occurs at 3- 6 months of age and lasts until 18 to 36 months of age. We report here on a 22- month-old child with THI and IgA deficiency, who had massive pneumococcal empyema. Her depressed IgG level returned to normal within 6 months, but IgA level was still low at 6 yr of age. Although THI is an age-dependent and self-limiting disorder, severe infection that includes an atypical presentation of an infection may occur in some patients and this requires evaluation with immunologic study.
Massive Empyema Associated With Transient Hypogammaglobulinemia of Infancy and IgA Deficiency
Park, Kuhn,Lee, Kyung-Yil,Lee, Mi-Hee,Lee, Joon-Sung,Kim, Ji-Chang The Korean Academy of Medical Sciences 2009 JOURNAL OF KOREAN MEDICAL SCIENCE Vol.24 No.2
<P>Transient hypogammaglobulinemia of infancy (THI) is originally defined as a physiological maturation defect of immunoglobulin G (IgG) production that occurs at 3-6 months of age and lasts until 18 to 36 months of age. We report here on a 22-month-old child with THI and IgA deficiency, who had massive pneumococcal empyema. Her depressed IgG level returned to normal within 6 months, but IgA level was still low at 6 yr of age. Although THI is an age-dependent and self-limiting disorder, severe infection that includes an atypical presentation of an infection may occur in some patients and this requires evaluation with immunologic study.</P>