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그레이브스병과 동반된 자가면역성 갑상선 질환 관련 뇌병증 1예
박경선 ( Kyoung Sun Park ),이신희 ( Shin Hee Lee ),조남열 ( Nam Yeol Cho ),최유아 ( Yu Ah Choi ),고윤명 ( Yun Myoung Ko ),남선우 ( Seon Woo Nam ),남수민 ( Soo Min Nam ) 대한내과학회 2016 대한내과학회지 Vol.91 No.2
A patient with encephalopathy associated with autoimmune thyroid disease (EAATD), which is one of the most important differential diagnoses of treatable dementia, presents with various neurological symptoms, such as repetitive epileptic seizures, altered mental status, and cognitive dysfunction. Steroid treatment is effective for EAATD. The incidence of EAATD increases considerably with age, particularly in female patients. Most patients with EAATD have normal thyroid function test results or mild hypothyroidism. Patients with EAATD with Graves’ disease are very rarely reported. Here, we report a case of a 63-year-old woman who complained of declining cognitive ability and ataxia. She was diagnosed with EAATD accompanied by Graves’ disease. Her neurological symptoms improved after intravenous steroid administration. (Korean J Med 2016;91:197-201)