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두빈-존슨 증후군 환자에서 동반된 급성 A형간염으로 인한 지속성 담즙 정체
라상호 ( Sang Ho Ra ),성세용 ( Se Yong Sung ),정호연 ( Ho Yeon Jung ),차재황 ( Jae Hwang Cha ),백순구 ( Soon Koo Baik ),조미연 ( Mee Yon Cho ),김문영 ( Moon Young Kim ) 대한소화기학회 2012 대한소화기학회지 Vol.59 No.4
Dubin-Johnson syndrome is a rare clinical entity. It shows intermittent symptoms such as chronic or intermittent jaundice, abdominal pain, weakness, nausea, vomiting, anorexia and diarrhea. Symptoms are precipitated or aggravated by pregnancy, alcoholism, surgical procedures and intercurrent disease. Chronic idiopathic jaundice is typical of Dubin-Johnson syndrome and its prognosis is good. We describe a case of prolonged cholestasis for more than 10 months caused by acute A viral hepatitis in a patient with Dubin-Johnson syndrome. It is a first report of cholestasis complicated by acute A viral hepatitis in a patient with Dubin-Johnson syndrome. (Korean J Gastroenterol 2012;59:313-316)
토혈을 동반하지 않은 대동맥식도누공의 내시경적 진단 1예
이종윤 ( Jong Yoon Lee ),장진석 ( Jin Seok Jang ),김동균 ( Dong Kyun Kim ),차재황 ( Jae Hwang Cha ),최원종 ( Won Jong Choi ) 대한소화기학회 2019 대한소화기학회지 Vol.73 No.1
Aortoesophageal fistula (AEF) is an extremely rare but lethal cause of massive gastrointestinal hemorrhage. Characteristic symptoms are mid-thoracic pain, sentinel minor hemorrhage, and massive hemorrhage after a symptom-free interval. Prompt diagnosis and immediate treatments are necessary to reduce mortality. However, AEF is difficult to diagnose because it is uncommon and often leads to death with massive bleeding before proper evaluation. We report a case of endoscopic diagnosis of AEF that did not present with hematemesis; it was treated with thoracic endovascular aortic repair (TEVAR) and surgery. A 71-year-old female presented to the emergency department with epigastric discomfort. Endoscopy demonstrated a submucosal tumor-like protrusion and pulsating mass with blood clots. Contrast-enhanced chest CT confirmed AEF due to descending thoracic aortic aneurysm. The patient immediately underwent TEVAR to prevent massive bleeding and subsequently underwent surgery. Endoscopists should consider AEF if they see a submucosal tumor-like mass with a central ulcerative lesion or a pulsating protrusion covered with blood clots in mid-esophagus during an endoscopy. (Korean J Gastroenterol 2019;73:35-38)