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정수택,지창하,정재용,김주홍,조혜제,노충희 인제대학교 1992 仁濟醫學 Vol.13 No.2
고환주위 횡문근육종은 드문 질환으로, 저자들은 최근 후복막강내 전이가 있었던 20세 환자에 대해서 수술, 화학요법 및 방사선 치료의 병합요법을 시행으로 16개월째 치료중에 있다. Rhabdomyosarcoma, derived from the unsegmented undiffentiated mesoderm, accounts for approximately 5~10% of all solid tumors in children. It is the most common soft tissue sarcoma in children younger than 15 years. Survival for children with rhabdomyosarcoma, like that for Wilms' tumor, has been greatly improved since the incorporation of chemotherapy into treatment program. With current miltidisciplinary regimens, the overall 2 year survival rate for children with rhabdomyosarcoma approaches 70%. A case of rhabdomyosarcoma with retroperitoneal metastasis is reported. A 20-year-old male was hospitalized because of scrotal mass, which was more enlarged after blunt trauma. At operation, paratesticular mass extending along the spermatic cord was removed. Pathologic finding of the tumor revealed rhabdomyosarcoma of embryonal type. Abdominal CT showed retroperitoneal metastasis. The patient has been treated with combined modality therapy for 16 months.