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최명훈 ( Myeung Hun Choi ),전지현 ( Jie Hyun Jeon ),손상욱 ( Sang Wook Son ),송해준 ( Hae Jun Song ),오칠환 ( Chil Hwan Oh ) 대한피부과학회 2006 大韓皮膚科學會誌 Vol.44 No.12
Nodular fasciitis is a benign, reactive, myofibroblastic, proliferative process of unknown etiology. It presents as a solitary, painless, rapidly-growing nodule over several weeks` duration. The condition is self-limiting, and proper diagnosis is essential to avoid unnecessary aggressive treatment. Diagnosis is often a challenge because nodular fasciitis may be confused with a malignant tumor due to its aggressive clinical behavior and histological features. It is most commonly located on the extremities and then the trunk. Such lesions also usually occur in middle age and are rarely diagnosed in childhood. We report a case of recurrent nodular fasciitis that arose from subcutaneous tissue on the back of a pediatric patient. (Korean J Dermatol 2006;44(12):1457~1459)
최명훈 ( Myeung Hun Choi ),전지현 ( Jie Hyun Jeon ),김애리 ( Ae Ree Kim ),오칠환 ( Chil Hwan Oh ),송해준 ( Hae Jun Song ) 대한피부과학회 2007 대한피부과학회지 Vol.45 No.3
Primitive neuroectodermal tumors (PNETs) are malignant, round-cell sarcomas which exhibit primitive neuronal differentiation. They usually arise in deep soft tissues, but occasionally bones and visceral organs are affected. In general, PNET presents as rapidly-growing, deeply located masses measuring 5~10 cm at their greatest diameter. Superficially located cases do occur but are rare. The typical PNET is composed of sheets or lobules of small round cells containing darkly-staining, round or oval nuclei. The cytoplasm is indistinct except in areas where the cells are more mature and elongated hair-like cytoplasmic extensions coalesce to form rosettes. We herein report a case of PNET that arose from subcutaneous tissue of the buttock in a 31-year-old woman. (Korean J Dermatol 2007; 45(3):275~278)
Human Tail의 임상양상을 보인 선천성 피부 평활근 과오종
신재빈 ( Jae Bin Shin ),전지현 ( Jie Hyun Jeon ),손상욱 ( Sang Wook Son ),송해준 ( Hae Jun Song ),오칠환 ( Chil Hwan Oh ) 대한피부과학회 2007 대한피부과학회지 Vol.45 No.3
A human tail is a rare congenital anomaly, and is characterised by a prominent lesion from the lumbosacrococcygeal region. Human tails are classified into ``true tails`` and ``pseudotails``. True tails are comprised of only mesenchymal tissue. They are presumed to be remnants of the embryologic tail. All other lumbosacrococcygeal protrusions are summarized as pseudotails. Congenital smooth muscle hamartoma usually presents as a well-circumscribed, hypertrichotic, hyperpigmented or skin-colored patch or plaque on the trunk or an extremity at birth. Histologically, numerous thick, long, well-defined bundles of smooth muscle fibers are scattered throughout the dermis in various directions. We report a case of congenital smooth muscle hamartoma in a 15-year-old male patient who presented with a tail-like protruding mass accompanied by hypertrichosis and underlying soft tissue deviation. (Korean J Dermatol 2007;45(3):287~289)