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폐 , 흉벽 , 중추신경계를 침범한 전신형 모균증 1 예
박수제(Su Je Park),정철원(Chul Won Jung),박언섭(Eon Sub Park),박애자(Ae Ja Park),이상재(Sang Jae Lee) 대한내과학회 1998 대한내과학회지 Vol.54 No.6
Disseminated mucormycosis is a rare but fatal fungal infection with a high mortality rate. Mucormycosis usually occurs in immunocompromised patients such as in patients with diabetes mellitus, leukemia, lymphoma and in patients undergoing anticancer therapy, prolonged immunosuppression, and antibiotic therapy. Early diagnosis and the resolution of predisposing factors, including the use of amphotericin B and wide surgical resection, are essential to make a successful outcome. We report a well-documented case of disseminated mucormycosis involving lung parenchyme, chest wall and central nervous system with the review, of literatures in patients with uncontrolled diabetes and Evans syndrome. Typical broad, branching in right. angle, non-septated hyphae were observed in the biopsy of the nodular mass on the anterior chest wall. Chest CT and brain MRI found three pulmonary cavitary lesions and multiple small nodules with ring-enhancement in the cerebrum, cerebellum and the brainstem. Although 1,116mg of amphotericin B in sum was given with flucytosine, she expired due to progressive mucormycosis.