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한국인 성인 Henoch-Schonlein Purpura에서 초기의 혈변과 신장 침범은 중요한 예후 인자
배창범 ( Chang Bum Bae ),이진우 ( Jin Woo Lee ),김현아 ( Hyoun Ah Kim ),정주양 ( Ju Yang Jung ),김한결 ( Han Gyeol Kim ),이미연 ( Mi Yeon Lee ),안선주 ( Seun Joo Ahn ),박혜린 ( Hae Lin Park ),이효진 ( Hyo Jin Lee ),강은정 ( Eun Ju 대한류마티스학회 2012 대한류마티스학회지 Vol.19 No.5
Henoch-Schonlein purpura (HSP) is a systemic vasculitis, characterized by small-vessel leukocytoclastic vasculitis with the deposition of immune complexes containing IgA. It is the most common acute vasculitic disorder affecting children but is relatively uncommon in adults. We investigated the clinical features and factors affecting the prognosis of adult HSP in Korea. Methods. From 1996 to 2011 seventy patients over 15 years of age with HSP were retrospectively analyzed. Results. Thirty eight patients (54.3%) were female and the age at disease onset ranged from 15 to 75 years (35.0±15.8 years). Purpuric skin rash was observed in all patients and arthralgia was present in 34 patients (48.6%). GI symptoms and kidney involvements were observed in 28 patients (40.0%) and 34 patients (48.6%), respectively. Complete remission was achieved in 46 patients (65.7%). The remission group showed a lower incidence of hematochezia (p=0.044), hematuria (p=0.008), and proteinuria (p=0.011) at diagnosis than the no remission group. About 10% of adult HSP patient progressed to chronic kidney disease (CKD), which showed higher a incidence of nephrotic range proteinuria. Only nephrotic range proteinuria at diagnosis was a significant risk factor for CKD (OR= 16.7, p=0.008, 95% CI=2.1∼133.1). Conclusion. Hematochezia, hematuria and proteinuria at the diagnosis of HSP are important prognostic factors in predicting remission. In addition, HSP patients with nephrotic range proteinuria at diagnosis have an increased risk of renal failure.