http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
방광 요관 역류를 동반한 Goldenhar 증후군 1례
안계현 ( Gae Hyun Ahn ),위영선 ( Young Sun Wee ),이규형 ( Kyu Hyung Lee ) 대한주산의학회 2007 Perinatology Vol.18 No.3
Goldenhar`s syndrome is a kind of congenital anomaly with epibulbar dermoid, preauricular skin tag, blind-ended fistula and vertebral anomaly. The primary cause is unknown but thought to be a structural developmental abnormalities of the 1st, and 2nd branchial arch. In this syndrome, we can observe characteristic anomalies of the face, ear, vertebrae, heart, and the nervous system. Treatment is surgical correction, removal of epibulbar dermoid, prevention of hearing loss through early hearing test. The consultations of ophthalmologist, otorhinolaryngologist, orthopedist and dentist are necessary for this syndrome. We report a case of Goldenhar`s syndrome with hemifacial hypoplasia, preauricular skin tags, blind-ended fistulas, hemivertebrae and vesicoureteral reflux.
재발성 세균성 뇌수막염을 동반한 특발성 접형골형 뇌류 1례
허혜영(Hae Young Hur),안계현(Gae Hyun Ahn),채규영(Kyu Young Chae) 대한소아신경학회 2007 대한소아신경학회지 Vol.15 No.1
저자들은 외상이나 수술 병력이 없는 환아에서 1년내에 2회의 세균성 뇌수막염이 발생한 후, 자세히 병력 청취를 하여서 뇌척수액 비루와 연관된 해부학적 기형을 의심한 후 발견된 특발성 접형골형 뇌류 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다. Encephaloceles are congenital defects in the skull through which menings and brain tissues herniated. Basal encephaloceles are found in 1 in 40,000 live births. Transsphenoidal basal encephaloceles are very rare, accounting for only 5% of all basal encephaloceles. Currently, most encephaloceles are diagnosed antenatally and present at birth. Postnatally, infants may present with CSF rhinorrhea, recurrent meningitis, headache, hypothalamicpituitary dysfunction. Some, particularly trasnssphenoidal encephaloceles are often clinically occult and diagnosis of the disease may be postponed up to adulthood. Surgical indications and approaches for transsphenoidal encephaloceles have been remained controversial. We report a case of CSF rhinorrhea and recurrent meningitis caused by transsphenoidal encephalocele.