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임화중(Hwa Joong Yim),백근욱(Keum Wook Baek),윤석부(Seok Bu Woon),장웅기(Woong Ki Chang),김동준(Dong Jun Kim),김홍기(Hong Ki Kim),채승완(Seung Wan Chae),박영의(Young Euy Park) 대한소화기학회 1994 대한소화기학회지 Vol.26 No.2
The Peutz-Jeghers syndrome is an autosornal dominant hereditary disease characterized by hamartous polyps of the gastrointestinal tract and by mucocutaneous melanin deposits. This syndrome is clinically important because of the complications caused by gastrointestinal pol- yps and of an increased risk for the development of cancer. W e experienced a case of develop- ing an adenocarcinoma of the stomach in patient with Peutz-Jeghers syndrome, who had mucocutaneous pigmentations and gastric, small intestinal and large intestinal polyps for seven years. (Korean J Gastroentero11994; 26: 337-342)