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나용호(Yong Ho Nah),김철우(Chull Woo Kim),김형곤(Hyung Gon Kim),이상곤(Sang Kon Lee),조정구(Chung Gu Cho),김학철(Hack Chel Kim),박양규(Yang Kyu Park) 대한소화기학회 1983 대한소화기학회지 Vol.15 No.2
N/A Rotor's syndrome is a familial disorder characterized by chronic, nonhemolytic, predominantly conjugated hyperbilirubinemia. The incidence of Rotors syndrome is very rare and only 11 cases were reported in Korea. Recently we observed three patients of Rotor's syndrome in two families. In these three cases, jaundice started at an early teenage and has shown a persistent but fluctuating course. The condition appeared compatible with normal life. These three patients of Rotor's syndrome had persistent elevation of the free and conjugated bilirubin and impaired ability to conjugate Bromosulphalein. The liver biopsy specimens were morphologically normal. The gallbladder were visualized on oral cholecytogram.