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Yin Yin Lee,Ping Chong Bee,Chew Kek Lee,Manimalar Naiker,Rokiah Ismail 대한피부과학회 2011 Annals of Dermatology Vol.23 No.-
Bullous pemphigoid (BP) has a recognized association with solid organ tumors, but is relatively rare in hematological malignancies. We report a 67-year-old male who developed BP after being diagnosed with myelodysplastic syndrome and refractory anemia with excess of blast (RAEB). Skin biopsy elucidated sub-epidermal bulla using direct immunofluorescence,revealing linear C3 and IgG deposits along the basement membrane. His BP was recalcitrant to the conventional treatment and only responded to a combination of high dose oral prednisolone and azathioprine. The relative refractory nature of his condition and concurrent RAEB supports a paraneoplastic nature. (Ann Dermatol 23(S3) S390∼S392, 2011)
( Yin Yin Lee ),( Ping Chong Bee ),( Chew Kek Lee ),( Manimalar Naiker ),( Rokiah Ismail ) 대한피부과학회 2011 Annals of Dermatology Vol.23 No.3s
Bullous pemphigoid (BP) has a recognized association with solid organ tumors, but is relatively rare in hematological malignancies. We report a 67-year-old male who developed BP after being diagnosed with myelodysplastic syndrome and refractory anemia with excess of blast (RAEB). Skin biopsy elucidated sub-epidermal bulla using direct immunofluorescence, revealing linear C3 and IgG deposits along the basement membrane. His BP was recalcitrant to the conventional treatment and only responded to a combination of high dose oral prednisolone and azathioprine. The relative refractory nature of his condition and concurrent RAEB supports a paraneoplastic nature. (Ann Dermatol 23(S3) S390~S392, 2011)